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B Bachy

Publications and source records attributed to B Bachy.

At least 37 records · Page 2Linked to original sources
PubMed1996

[Aniridia and Wilms tumor: 2 cases of fetal rhabdomyomatous nephroblastoma].

BACKGROUND: Wilms tumor is associated in 7 to 10% of patients with congenital abnormalities. Among those, aniridia is the most constant feature of the WAGR syndrome that includes, in one third of cases. Wilms tumor. We report two cases of aniridia associated with fetal rhabdomyomatous nephroblastoma. CASE REPORTS: Case 1. A one-year old girl with congenital aniridia was admitted for macroscopic hematuria. Abnormal ultrasonography and tomodensitometry revealed a large, bilateral, kidney tumor. The patient was given actinomycin and vincristine, without efficacy. Bilateral tumorectomy was performed 6 months later and the histological study showed a fetal rhabdomyomatous nephroblastoma. This patient is in remission at the age of 5. Case 2. A boy, also with congenital aniridia, presented with macroscopic hematuria at the age of 2 years revealing a nephroblastoma located on his right kidney. Preoperative chemotherapy remained uneffective and the nephrectomy performed 1 month later permitted the diagnosis of fetal rhabdomyomatous nephroblastoma. The patient is well 4 years later. CONCLUSION: Both cases of fetal rhabdomyomatous nephroblastoma, a histological variant of Wilms tumor, seem to be the first reported in the WAGR syndrome.

Aniridia↗
PubMed1996

[Perirenal necrotic and cystic pseudotumors in children. Report of two cases].

This work describes two cases of necrotic, encysted pseudotumors of unknown origin, in children; the lesions located on the anterior side of the kidney, near its inferior pole were remarkable for their size and their numerous adhesions to adjacent structures. The hypothesis of an initial infectious or tumoral mechanism are discussed, particularly the similarities supported by both lesions with the regressive patterns of some neuroblastomas.

Child↗
PubMed1994

[Popliteal pterygium syndrome. A exceptional case].

We report the case of a patient with a popliteal pterygium syndrome, a rare malformation associating, in its complete form, cleft lip and cleft palate, cleft lower lip, intergingival synechia, defects of the genito-urinary tract and popliteal pterygium. Based on this observation and a review of the literature, the phenotypic and genotypic aspects of this malformation were discussed together with adapted therapeutic management and genetic counselling.

Abnormalities, Multiple↗
PubMed1993

[Obstructions in children].

In matters of intestinal obstruction the younger the child, the clearer the features of this condition. As in adults, obstruction reveals an intestinal blockage related to multiple and varied origins. Neonatal obstruction deserves special attention, as it often reveals a digestive tract abnormality with interrupted continuity which is incompatible with life unless the appropriate surgical treatment is carried out. Constant advances in intensive care and nutritional care of these infants result in increasingly "borderline" digestive situations, but certain situations have not yet been solved in the absence of success of intestinal transplantation.

Age Factors↗
PubMed1991

Pancreatoblastoma: response to chemotherapy.

Two cases of pancreatoblastoma in children are reported here. Only biopsies were made at laparotomy as surgical resection by duodeno-pancreatectomy was not possible. In both children a dramatic response was observed with chemotherapy: doxorubicin plus cisplatin for one, cyclophosphamide, actinomycin D, bleomycin, vinblastine sulfate, and cisplatin for the other. After completion of the chemotherapy the first patient had a local resection; then he had radiotherapy. He is alive in first remission 40 months after the end of the treatment. In the second patient, regional recurrence occurred 8 months after chemotherapy was ended. A transient second remission was obtained with ifosfamide plus etoposide alternating with epirubicin plus vincristine. The patient died 36 months after the diagnosis. Therefore, these two cases suggest that chemotherapy may be proposed before any attempt at surgical excision. Nevertheless, early consolidation by radical resection or irradiation must be considered.

Adenocarcinoma↗
PubMed1990

[Has the Ilizarov technique come of age in pediatric orthopedics?].

The Ilizarov method can be used for several applications: limb lengthening correction of axial malignement, pseudarthrosis, traumatology and in several sites: leg, foot, knee, femur, forearm and arm. The authors recall the principles and possibilities of this method and give details about its utilisation for each indication, and for their preferred indications: lengthening for marked disparity, complex trauma, progressive distraction of soft tissues, and for very young children.

Adolescent↗
PubMed1989

[Surgical indications for hydronephrosis discovered antenatally].

The authors report series of 82 hydronephrosis (in 70 infants), detected antenatally by ultrasound. The cases were classified in 3 groups according to the severity of pelviureteric junction obstruction. Only the more severe cases are operated at once. In the remaining cases the observation help to decide the indications. In this series 35 renal units among 82 have been operated at date. The 47 remaining are annually followed up by ultrasound.

Female↗
PubMed1988

[Fibromatosis in children: regression with prolonged chemotherapy. Apropos of 2 cases].

Surgical excision is the usually recommended treatment of Fibromatosis in children. However the invading nature of this tumor is responsible for recurrences leading to mutilating surgery and eventually to death despite the histologically benign appearance. We observed two cases of decrease under lengthy chemotherapy. In the first case, a 4-year-old boy with a huge abdominal wall tumor had two biopsies leading to the diagnosis of fibromatosis. The tumor measured 15 x 14 x 10 cm, and compressed the right ureter when chemotherapy was started. Actinomycin 1,500 microgram/m2 at Day 1 and vincristine 1.5 mg/m2 at Day 1 and Day 8. This courses were repeated every four weeks. Tumor decreased slowly but constantly. After 17 months it measured only 5 cm in diameter. The biopsy confirmed the nonprogressive nature of the residual fibromatosis. In the second case, a 12-year-old boy had a tumor of the left anterior thoracic wall. The histologic study diagnosed a fibromatosis. Two courses of IVA (ifosfamide, vincristine, actinomycin), did not lead to any decrease. A wide excision was achieved but left invaded edges. Then the child was treated by actinomycin 750 microgram/m2 at Day 1 and vincristine 1.5 mg/m2 at Day 1 and Day 8, one course every four weeks during ten months. At this time biopsies revealed a scar without progressive fibromatosis. This two cases show the interest of a chemotherapy in extensive fibromatosis. A mild treatment but for a long time seems to succeed where more intensive courses have failed.

Abdominal Muscles↗
PubMed1988

[Ambulatory anesthesia in pediatrics. 2-year experience of performance at a day hospital].

Ambulatory pediatric anaesthesia is done within a well-organized medical and surgical structure. The anaesthesia consultation confirms the surgical indications, taking into account certain medical pathologies. 27% of elective surgery is done in day-hospital. The anaesthetic techniques described have been done in children from three weeks to sixteen years of age. Intubation was not an exclusion criterion. The major causes for transfer to the general hospital (2.9%) are given. Anaesthetic complications represent 0.1% of such transfers. Scrupulous respect of the selection criteria, competence of anaesthesiologists and of pediatric surgeons are prerequisites for good results.

Ambulatory Surgical Procedures↗
PubMed1988

[Conservative treatment with high anastomosis in duplications with lesions of the upper kidney pelvis].

High anastomoses (ureteropyelic or uretero-ureteral) were performed in 14 patients for either ectopic ureter (7 cases) or uterocele (7 cases). This simple operation (one benign complication) allows conservation of a still functioning upper segment. In cases of ureterocele, aspiration of the latter eradicates it but the high operation does not treat the possibly associated reflux. Certain secondary operations are therefore necessary (2 of the 7 cases). Means for assessing upper segment function (particularly renal scan) are discussed, the presence of function justifying the conservation of this segment even if it is dysgentic and sometimes the site of nodular renal blastema. The respective indications for high anastomosis and total bladder surgery are discussed.

Adolescent↗
PubMed1987

[Undescended testicles: 2-stage reduction or Fowler's technic. Apropos of 2 comparative series].

The testicular vessel transection allows a one-stage orchidopexy for high undescended testes. The authors have been using this procedure (as described by Fowler) since january 1984. 29 operations have been performed in this way. This series is compared to another series of 28 staged orchidopexies, a procedure which was used in Rouen until december 1983. The number of cases in each series is not high enough to allow a significant comparison; no conclusion can be drawn as for the long term result concerning the testicular function. However the procedure described by Fowler has the great advantage of being performed in one-stage. But the surgeon must comply with strict rules and the authors point out the difficulties of the operation.

Child↗
PubMed1987

[Intestinal stenosis, sequelae of necrotizing enterocolitis. Analysis of 9 cases].

Intestinal necrosis was a complication of necrotizing enterocolitis of the newborn in 9 of 42 cases. In 6 neonates it followed medical treatment of the enterocolitis, presenting in this case as an occlusive syndrome. After surgical treatment (3 cases) the diagnosis was made from radiologic imaging prior to reestablishment of digestive continuity. Surgery was necessary in all cases, and procedures used are described (technic, date of operation). The prognosis of enterocolitis is worsened by this stenosis (1 death in the 9 cases).

Enterocolitis, Pseudomembranous↗