[The Weill-Marchesani syndrome. Apropos of 2 further cases].
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Biomedical subjects
Publications and source records attributed to C Fauchier.
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The purpose of this work was to evaluate the genetic propensity importance in the monoclonal gammapathies occurrence. Systematic serum-electrophoreses were performed on 172 relatives of 37 reported patients and on 10,784 controls over 30. The 4 families including one or more "paraproteinemia" other than the proband's were investigated. Experimental, epidemiologic, immunologic and genetic arguments are discussed.
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An IgGK monoclonal gammopathy occured in two patients with streptococcus viridans bacterial endocarditis. The gammopathy has been unchanged, respectively for 32 and 21 months following its detection. The alternate physiopathologic hypothesis are argued.
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