Cardiac arrhythmias and the adult form of type II glycogenosis.
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Adult↗
Biomedical subjects
E Auff
Publications and source records attributed to E Auff.
Spinal cavernous haemangioma (intradural-extramedullary) underlying repeated subarachnoid haemorrhage.
Within a period of 13 months a 24-year-old male student experienced four attacks of subarachnoid haemorrhage. An intradural-extramedullary haemangioma at the level of the second thoracic segment was found to be the cause of the repeated bleeding.
Adult↗
Cerebellar glioblastoma presenting clinically as Wallenberg's syndrome.
The clinico-neuropathological report is given of a glioblastoma multiforme with primary site in the cerebellum. The patient presented clinically with Wallenberg's syndrome; morphological investigations revealed the tumor partly invading the dorsolateral region of medulla oblongata. There are some reports of Wallenberg's syndrome not caused by vascular stenosis or occlusion, but by metastatic tumors in the lateral medullary region. The present report is the first of a cerebellar glioblastoma causing the peculiar brainstem syndrome.
Cerebellar Neoplasms↗
[The Steel Richardson Olszewski-syndrome. A report on 3 further cases (author's transl)].
In this report we are describing 3 further cases of progressive supranuclear palsy, all displaying the typical clinical features (first described by Steele, Richardson and Olszewski, 1964): Ophthalmoplegia (affecting chiefly vertical gaze), pseudobulbar palsy, dysarthria, dystonic rigidity of the neck and upper trunk and dementia. Clinical symptoms started between 49 and 51 years of age with slow progression during 2 to 4 years. One patient died 2 years after the first clinical symptoms began. The purpose of this paper is, to describe a further group of 3 cases of progressive supranuclear palsy and to point out in detail the clinical symptoms, that all correspond to supranuclear localisation of this disease and to report about some differences in the development of the disease and the fully developed disorder. The use of treatment with Adamantin and Akineton was not (very) satisfying.
Amantadine↗
[Primary diffuse leptomeningeal melanoblastosis and its CT appearances (author's transl)].
We report the case of a twelve-year-old boy who died, after a six months history, from primary diffuse leptomeningeal melanoblastosis, CT investigations showed a saw-tooth contrast enhancement at the brain surface. CT investigations may therefore be very helpful in meningeal lesions - apart from the importance of CSF investigations.
Autopsy↗
[Giant connatal glioma (author's transl)].
A clinico-neuropathological report is given on a four months old girl with head enlargement first recognized at the age of four weeks. A giant intracranial tumor was found at autopsy, which was histologically an isomorphous, largely pilocytic astrocytoma without morphological features suggesting rapid growth. This connatal astrocytoma seems unique in size, suggesting tumor formation already during very early embryonal development.
Astrocytoma↗
MR of cerebral Whipple disease.
A case of cerebral Whipple disease is reported. MR findings of the brain are discussed in relation to neuropathologic lesions reported previously. Repeated MR investigations may serve as a valuable tool to evaluate long-term efficacy of treatment in cerebral Whipple disease.
Atrophy↗