PubMed HealthSearch

Biomedical subjects

F H Verhey

Publications and source records attributed to F H Verhey.

4 recordsLinked to original sources

Benign (nonparoxysmal) familial chorea of early onset: an electroneurophysiological examination of two families.

A nonparoxysmal nonprogressive autosomal dominant choreatic disorder of early onset is described in two families. Laboratory investigations of blood, urine and cerebrospinal fluid were normal. Extensive electroneurophysiological examinations did not reveal evident abnormalities. The contingent negative variation was also normal, except for a P500. These electroneurophysiological data are the opposite of what can be found in cases of Huntington's chorea.

Child

Autosomal dominant paroxysmal kinesigenic choreoathetosis. An electroneurophysiological study.

A case of an 11-year-old boy with an autosomal dominant form of paroxysmal kinesigenic choreoathetosis is presented. Routine EEG, sleep EEG recording, and registration of visual evoked potentials and somatosensory evoked potentials were normal. EEG with videomonitoring and registration of event-related potentials, however, showed abnormalities, which are discussed in detail. Our data provide further arguments in support of the hypothesis that paroxysmal kinesigenic choreoathetosis is the expression of a dysbalance in the cortico-striopallidal-thalamic loop, and has an extrapyramidal genesis.

Athetosis