[Abnormal pulmonary venous return].
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Biomedical subjects
Publications and source records attributed to J Ferrané.
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The authors describe 18 cases of this syndrome and emphasize that attenuated clinical forms of homozygotic drepanocytosis exist, as well as, in a more general manner, in acute drepanocytic syndromes. The disease may first appear in adult life. The frequency of radiological signs in the spine has to be stressed, and the authors emphasize the diagnostic value of the "staircase" deformation of the vertebrae, representing the sequelae of bone ischemic lesions. The discovery of this radiological sign suggested the diagnosis of a hemoglobinopathy in two cases. This attenuated form of the disease presents the same risks of thromboses but these complications can be reduced by prophylactic treatment. This underlines the need for early detection and radiological investigation can be of great assistance.
Abdominal or thoracic aneurysms can be perfectly well visualized by computed tomography, and tumors lying close to the aorta and simulating ectasia can often be eliminated. The exact topographical features of the lesions can be defined as well as their extension superiorly. In many cases, calcifications, clots, a permeable channel, or even a periaortic hematoma showing fissuration can be demonstrated. On many occasions the value of computed tomography is such that angiography may not be necessary.