PubMed Health⌕ Search

Biomedical subjects

J García Consuegra

Publications and source records attributed to J García Consuegra.

10 recordsLinked to original sources

[Dermatomyositis in children: clinical course of 9 cases].

Eight cases of dermatomyositis and one of polymyositis were studies among five male and four female patients. All had criteria definitive of the disease. All nine patients were give prednisone; six of them responded favorably to treatment and after discontinuing still remain asymptomatic. Three male patients have had a worse response to therapy, two of them deceased and the third still remains symptomatic, but very slowly improving after fourteen months with steroids and cyclophosphamide. These three patients have had chronic cutaneous vasculitic ulcers and this is a sign of bad prognosis. Both deceased patients exhibited important visceral complications (digestive and pulmonary). A more aggressive therapy has been suggested in these forms of worse clinical evolutions, including use of immunosuppressors.

Child↗

[Pathology of the phagocytic mononuclear system. Apropos of 4 cases].

Four patients, with disorders belonging to mononuclear phagocyte system diseases are described: a case of malignant histiocytosis; one of Weber-Christians disease and two siblings affected by familiar erythrophagocytic lymphohistiocytosis. An attempt is made to update classification of this group of diseases previously known as reticulosis, reticulohistiocytosis, reticuloendotheliosis, etcetera.

Child↗

[Three cases of mucolipidosis type III (author's transl)].

Three cases of mucolipidosis type III in three siblins ranging in age from 4 to 10 years are reported. One of them was severely involved; the other two in a lesser degree. The enzymatic studies performed are exposed, together with a discussion and interpretation of the findings. The concepts regarding the group of metabolic diseases among which mucolipidosis is nowadays included are reviewed. Some characteristics of the enzymatic disorder, origin of the disease, are finally commented.

Child↗

[Two cases of secondary amyloidosis (author's transl)].

Two cases of secondary amyloidosis are presented. Both cases presented as nephrotic syndrome and were confirmed by biopsy dying two years later of the appearance of proteinuria. Incidence and characteristics of amyloidosis in infancy is commented.

Amyloidosis↗