[Sonographic diagnosis of a choledochal cyst in a child].
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Biomedical subjects
Publications and source records attributed to K A Vergesslich.
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The case history of a 12 months old boy with recurrent pneumonia following ingestion of cow's milk is described. After receiving cow's milk containing formula he presented with fever, tachypnea, diffuse rales and crepitations over both lungs. The chest X-ray revealed marked bilateral alveolar shadows. A high titer of antibodies against the four major antigenic components of cow's milk protein was demonstrated by Ouchterlony's precipitation test and the fluorescent immunosorbent test. Withdrawal of cow's milk from the diet resulted in complete resolution of clinical and radiological findings.
Insertion of extracardiac right ventricular (RV)-pulmonary artery (PA) conduits for repair of severe forms of RV-PA discontinuity has become a widely used technique. During a 10-year period, 76 patients had open heart repair with a porcine-valved RV-PA external conduit. The most common diagnoses were truncus arteriosus (15%) and pulmonary atresia with ventricular septal defect (15%). The patients were 18 days to 37 years old (median 7 years). The postoperative median follow-up period was 4 years. Four patients (8%) have been lost to follow-up. Nineteen patients (25%) died in the early postoperative period and there were 10 late deaths (13%). Calculated probability of survival was 66% at 8 years. Thirty-six patients have undergone late hemodynamic studies. A residual shunt was present in 14% of the patients; moderate to severe PA hypertension was present in 25% and significant RV-PA gradients (greater than 30 mm Hg) in 50%. The mean RV pressure for the group was 78.5 +/- 38 mm Hg. The severity of the gradients appeared to be greater in patients who had been followed longer. Ten patients have undergone reoperation because of conduit obstruction or residual shunting; 6 are alive and well. Of the surviving patients, 95% are acyanotic and without significant exercise intolerance and only 5% have cardiovascular symptoms. Thus, open heart repair using an external RV-PA conduit provides a marked improvement in the quality of life in patients who survive.
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An 11-year-old girl developed typical symptoms of bird breeder's lung after several years of contact with budgerigars and other birds. The clinical diagnosis was confirmed by immunological and lung-function tests. Despite exclusion of exposure to allergens and treatment with steroids and D-penicillamine no improvement occurred, the exogenous allergic alveolitis progressing to fibrosing alveolitis of which the girl died.
During the past half of this century there has been a tremendous development of chemical products. Their application in every day life is widespread, and problems arose summarized under the term of civilisation damages. An important aspect is the effect of detergents on human skin. Every day more than 100 million people have contact with surface active substances--an influence on the physiologic steady state of the skin or its protective mechanisms was thought to be possible. After reviewing the relevant literature of the past ten years following conclusions can be drawn: As to the problem of tolerance we can say that there is no objection against the use of anionactive detergents. Under extreme conditions, e.g. constitutional anomalies, or intense application on previously damaged skin, injury of the skin can be observed. In the age group between 6 and 12 years there exists no difference in the resistance against alkali or acids in comparison to adults. It has not been demonstrated yet, however, whether the buffering capacity is already active in the skin of the newborn, or when it becomes effective after birth. We can recommend the use of modern detergents in pediatrics, they represent an important part of modern hygiene in childhood, especially in infancy. For optimal efficacy one has to adjust the substance to every constitutional skin type and to preexisting skin damages.
Autoimmunhemolytic anemia in childhood can be divided into two main groups according to the length of the illness: an acute, transient form and a chronic, prolonged one. The etiopathology of the illness is still unknown. It is most postable that there is a connection with virus infections, whereby the antibodies, appearing within the framework of an immunological reaction, are to be considered as a secondary response to the infection. It could not, unfortunately, be proved in the case of our patient that there had been a virus infection. The role of immunodefects in the case of the acute form is currently being discussed in the more recent literature and the point als made that genetic defects are possible in the connection.
In children with growth retardation and the typical face, particularly with valvar pulmonary stenosis, the Noonan syndrome is the be suspected. In early infancy, these patients show very severe developmental retardation and muscular hypotony. Mental retardation is frequent but not compulsory. The most important diagnostic tool is the chromosomal analysis. In our patient, the syndrome was diagnosed becaused of the typical appearance and the angiocardiographic findings in connection with a normal chromosomal sequence.