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Biomedical subjects

M C Mouren

Publications and source records attributed to M C Mouren.

9 recordsLinked to original sources
PubMed1979

[Recent data on Lafora disease. Apropos of 17 cases].

This study reviews 99 anatomically verified case of Lafora body disease (82 from the literature and 17 personal cases). The clinical symptoms of the disease are characterised by the triad; epilepsy, myoclonus and dementia. An anatomical and histochemical study has been undertaken and as a result emphasis is given to recent hypotheses that suggest there are similarities with Type IV glycogen storage disease (Andersen's disease) which, although clinically distinct, has the same enzyme defect.

Adolescent↗
PubMed1978

[Depression in the child: Clinical and psychopathological aspects].

The present work is exclusively about depressions in childhood till the end of latency (11--12 years old children). It serves a double purpose: to try and show that children from their earliest childhood can be subject to feelings of sadness, moodiness, dismay, self-depreciation; to facilitate, through a better clinical and psychological knowledge, diagnoses in (cases of) depressions. In the first part, we shall study the different clinical forms of depressive states, their factors and their evolution. Three cases of personnal observations will illustrate those theoretic data. The relations between suicide and depression are introduced in the second part of this work. Finally, the authors will tell about the main psychanalytic works which permit to progress towards the recognition of the central function of the depressive phenomena in the structure of a personnality.

Bipolar Disorder↗
PubMed1977

[Vagrancy: psychological and psychopathological aspects].

The authors, after defining the words "vagrancy" and "vagrant", explore their semantical field and try to specify differences in respect of neighbouring words, often confused with them. An historical sketch of vagrancy, from antiquity to the present era, is depicted. There after, the authors state the evolution of theories of vagrancy, from the biological, psychological, psychiatrical and sociological points of view. The last part of the paper considers psychopathology of vagrancy, specially in psychoanalytical and phenomenological approaches, and problems of rehabilitation.

Adult↗
PubMed1976

[Post emotional syndromes (author's transl)].

On the basis of ten clinical cases of post emotional shock, the following aspects are discussed: the causal emotion and its characteristics, its psychological repercussions and the mechanisms involvent, the clinical patterns observed, both somatic and psychic, and their interpretation. Attention is called to the consequences of such emotions from the forensic view-point and the need to ascertain and specify the nature and intensity of the emotional trauma and the actual state of anxiety. Emphasis is laid on the difficulty of making expert appraisals and fixing equitable compensations, as experts differ and their approaches to the problem and also because of the functional character of sequela and their varying degree of severity.

Accidents, Occupational↗
PubMed1975

[Tumors of the glomus jugulare].

Tumours of the glomus jugulare always raise diagnostic and therapeutic problems. We decided to review the pathology and clinical findings whilst reporting a typical case found on our neurology unit. After a brief review of the embryology, anatomy and histology of the glomus jugulare, the authors report the case of a patient who presented a recurrent intracranial form with involvement of several cranial nerves, together with associated involvement of the carotid glomus. This was a familial disease. The patient was operated on with excellent results. The authors then present a clinical description of the various signs in glomus tumours,; depending more on the origin of the tumours than on the length of history. They then criticize the diagnostic interest of radiology, emphasizing the interest of angiography which may demonstrate a pathological vascular focus derived from the internal carotid artery together with the vertebro-basilar system. Retrograde jugulography also provides important information. The treatment of glomus jugulare tumours is, above all, surgical. They are approached through the ear in order to localise the intra-petrous part, or else, they may be approached through the skull. A combined otological and neuro-surgical approach to sometimes necessary for the lesion may involve both the petromastoid region and the posterior cerebral fossa. Radiotherapy is often advised after operation, in view of the importance of the vascular component of these tumours. The results of treatment are, on the whole, satisfactory.

Female↗
PubMedDate not supplied

[Lafora disease (author's transl)].

On the basis of 21 personal observations as well as those (82) from the litterature, it is concluded that the progressive myoclonic epilepsy with Lafora bodies (P.M.E.) constitutes a disease on its own. The clinical features are those described in the litterature observations and completed by some characteristics; the high frequency of visual symptoms (47 p. 100 personal cases); the relatively less bad evolution of epilepsy, perhaps in relation with use of modern drugs; the relatively moderate intensity of myoclonus which becomes complete only at the end of the evolution. From E.E.G. point of view, we can distinguish three periods: an initial one at the very onset of disease, who will show the same features as observated in primary generalized epilepsy, i.e. a well preserved background activity with superimposed generalized fast spikes and waves facilitated by the I.L.S. Then follows a period of evolutive E.E.G. (1-2 years after the onset of the disease) characterized by progressive slowing of the posterior background, enlargement of posterior slow activity and appearance of diffuse theta and delta activity. Simultaneously spikes and waves are taking less typical and bisynchronous aspect. Finally after 3 to 5 years from the onset there is a diffusely slow E.E.G. with superimposed fast multiple spikes. The E.E.G. findings in litterature usually refer only to this last period (stationary or terminal period). Occipital independent multiple spikes are frequently observed and could correlate with the visual symptoms observated in the Lafora disease. Some elements of differential diagnosis are given with respect to primary generalized epilepsy at the onset of the disease and later on with respect to dyssynergia cerebellaris myoclonica and to the progressive myoclonic epilepsy without Lafora bodies.

Adolescent↗