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Biomedical subjects

N Beail

Publications and source records attributed to N Beail.

7 recordsLinked to original sources
PubMed1989

Dietary treatment of hyperlysinaemia.

We describe the lysine restricted, dietary management of three out of four siblings who were identified as having hyperlysinaemia. The diets, started in the neonatal period, were maintained for varying periods with unpredictable success. The propositus, who was not treated, was diagnosed at the age of 5 years, by which time he was already severely handicapped, presumably because of his metabolic disorder. Tentative recommendations are put forward for the management of this seemingly rare disorder. Mild chronic ammonia toxicity may be a factor in the pathogenesis of this condition.

Amino Acid Metabolism, Inborn Errors↗
PubMedDate not supplied

A comparative study of profoundly multiply handicapped children's scores on the Bayley and the Griffiths developmental scales.

Twenty-five profoundly multiply handicapped children were tested using both the Bayley and the Griffiths scales by the same psychologist, who did not have prior knowledge of their medical and social histories. Scores obtained from the Griffiths scales were consistently higher than those obtained from the Bayley scales. The intercorrelation between the two tests was high. These results suggest that although the two tests may be used interchangeably, their numerical scores are not equivalent when administered to this population.

Adolescent↗
PubMedDate not supplied

The nature of interactions between nursing staff and profoundly multiply handicapped children.

The rate and content of naturally-occurring interaction patterns between nursing staff and profoundly multiply handicapped children were observed within a long-stay ward in a large mental handicap hospital. Child behaviours were recorded as appropriate, inappropriate or neutral and responses to the target child's behaviour were coded as positive attention, negative attention and no attention. It was found that for more than half of the time (54%) that the children were observed, they were doing nothing. Staff interacted with them for 16.2% of the total observation period. Most of the attention given by staff was positive, regardless of the appropriateness of the child's behaviour. A social learning framework suggests that given the low rate of interaction, potential therapeutic opportunities are being missed and the style of those interactions which occur may be anti-therapeutic. The implications of these findings for nurse training and hospital management are discussed.

Adolescent↗
PubMedDate not supplied

Evaluation of a staffed ordinary house for children with severe learning difficulties.

The concept of living in an ordinary house in an ordinary street is becoming well accepted by those providing services to people with mental handicaps. Numerous examples have been described, but little in the way of service evaluation has been done. It is important to demonstrate that the quality of life is better in 'smaller units' and that institutional patterns of care are not being reproduced in the community. An observational study of small homely units for adults with mental handicaps has been carried out and has shown that the quality of life is better. This paper reports an observational study of the quality of care in a small staffed house for children with severe learning difficulties. The rate and content of naturally occurring interaction patterns were observed. The Child Management Practices Questionnaire was also administered. The results show that these children are enjoying a better standard of care than that found in hospital studies. However, some management practices were found to be institutionally orientated. For example, there was restricted access to some areas of the house, a lack of personal possessions and staff served and supervised meals rather than eating with the children. The implications of the findings are discussed in relation to recent policy trends and alternative forms of care in the community.

Adolescent↗
PubMedDate not supplied

Assessing knowledge.

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Community Health Nursing↗