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PubMed · 10230118

[A uterine pecoma: a case report].

V D'Andrea·G Lippolis·F Biancari·L P Ruco·A Marzullo·B M Wedard·F M Di Matteo·R Sarmiento·A Dibra·E De Antoni
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Abstract

The authors describe the first ever reported case of a malignant pecoma of the uterus infiltrating the ovary, the tube and two bowel loops. This extremely rare tumour usually shows a benign behaviour and seems to arise from the perivascular epithelioid cells (PEC).

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Epithelioid CellsFemaleHumansIntestinal NeoplasmsIntestine, SmallMiddle AgedMuscle NeoplasmsNeoplasm InvasivenessOvarian NeoplasmsTerminology as TopicUterine NeoplasmsCase ReportsEnglish AbstractJournal Article

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V D'Andrea, G Lippolis, F Biancari, L P Ruco, A Marzullo, B M Wedard, F M Di Matteo, R Sarmiento, A Dibra, E De Antoni. 1999. [A uterine pecoma: a case report].. https://pubmed.ncbi.nlm.nih.gov/10230118/

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We report the clinicopathologic, immunohistochemical and ultrastructural features of two unusual tumors of the uterus composed of spindle and epithelioid cells strongly positive for HMB45. The two patients of 56 and 48 years of age had, respectively, hemoperitoneum and abnormal uterine bleeding. Morphologically, both tumors showed atypia and extensive necrosis. The neoplastic cells express immunohistochemically both melanogenesis (HMB45) and smooth muscle markers (actin). Ultrastructural analysis showed the presence of intracytoplasmic membrane-bound granules. We viewed these neoplasms as perivascular epithelioid cell (PEC) tumors with aggressive features. Follow-up has shown the death of one patient whereas the other is alive without disease 36 months after the surgery. The two patients were evaluated for signs of tuberous sclerosis complex, and findings were negative.

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