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PubMed · 10752112

Malignant spinal neurofibrosarcoma.

R Kett-White·J L Martin·E W Jones·C O'Brien
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Abstract

STUDY DESIGN: A report of a case of metastatic spinal neurofibrosarcoma. OBJECTIVE: To document metastatic neurofibrosarcoma as a cause of spinal cord compression and to review the literature. SUMMARY OF BACKGROUND DATA: Three previously reported cases of metastatic neurofibrosarcoma of the spine were reviewed. METHODS: The patient's clinical record and radiologic investigations as well as the result of a search of the English literature are reported. Magnetic resonance images, computed tomographic scans, and histology photomicrographs are displayed. RESULTS: Paraparesis developed in this patient, due to a posterior extradural thoracic spinal cord compression by a neurofibrosarcoma believed to be metastatic from a neurofibrosarcoma of the femoral nerve. CONCLUSIONS: Malignant spinal metastasis remains a rare complication of neurofibromatosis, with a very poor prognosis.

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Fatal OutcomeHumansLaminectomyMagnetic Resonance ImagingMaleMiddle AgedNeurofibromaNeurofibrosarcomaSoft Tissue NeoplasmsSpinal Cord CompressionSpinal Cord NeoplasmsTomography, X-Ray ComputedCase ReportsJournal ArticleReview

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BibTeXRIS

R Kett-White, J L Martin, E W Jones, C O'Brien. 2000-03-15. Malignant spinal neurofibrosarcoma.. https://doi.org/10.1097/00007632-200003150-00019

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