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PubMed · 10830014

Juvenile dermatomyositis.

V Seth·S K Kabra·O P Semwal·Y Jain
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Abstract

The clinical profile of 7 children and their follow-up is described. There was female preponderance with mate to female ratio of 1:6. The median age of onset was 6 years. All the patients had skin rash, muscle weakness and abnormal enzyme profile. Muscle biopsy was performed in 6 and was abnormal in all of them. The electromyogram (EMG) was performed in 6 and was found abnormal in five. All the children responded well to corticosteroids. Two children received intravenous dexamethasone bolus and showed good response.

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Adrenal Cortex HormonesAge FactorsBiopsy, NeedleChildChild, PreschoolDermatomyositisElectromyographyFemaleFollow-Up StudiesHumansIndiaMaleSurvival RateClinical TrialJournal Article

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V Seth, S K Kabra, O P Semwal, Y Jain. Juvenile dermatomyositis.. https://doi.org/10.1007/bf02751533

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