Brachial plexopathy associated with diffuse edematous scleroderma.

L Mouthon; C Halimi; J C Dussaule Md; M Cayre-Castel Md; L Guillevin

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PubMed · 10922959

Brachial plexopathy associated with diffuse edematous scleroderma.

L Mouthon·C Halimi·J C Dussaule Md·M Cayre-Castel Md·L Guillevin

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Abstract

Peripheral nervous system (PNS) involvement is rare in systemic sclerosis (SSc), usually restricted to peripheral nerve entrapment. To our knowledge, only one case of scleroderma with brachial plexus involvement has been reported previously. We report here on a 61-year-old woman with past history of limited cutaneous SSc who developed motor deficiency in the left arm concomitant with diffuse edematous scleroderma without evidence for trauma or compression of the brachial plexus. After six months intravenous pulse cyclophosphamide therapy, dramatic improvement of skin and neurological involvement was observed.

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Anti-Inflammatory Agents Brachial Plexus Neuropathies Cyclophosphamide Disease Progression Drug Therapy, Combination Female Humans Immunosuppressive Agents Middle Aged Motor Skills Prednisone Scleroderma, Localized Scleroderma, Systemic Case Reports Journal Article

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L Mouthon, C Halimi, J C Dussaule Md, M Cayre-Castel Md, L Guillevin. 2000. Brachial plexopathy associated with diffuse edematous scleroderma.. https://pubmed.ncbi.nlm.nih.gov/10922959/

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