[Pigmented villonodular synovitis. Diffuse and localized forms in children].

D Rosenberg; R Kohler; E Chau; R Bouvier; J M Pouillaude; L David

doi:10.1016/s0929-693x(00)00214-1

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[Pigmented villonodular synovitis. Diffuse and localized forms in children].

D Rosenberg·R Kohler·E Chau·R Bouvier·J M Pouillaude·L David

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Abstract

UNLABELLED: Pigmented villonodular synovitis (PVS) is characterized by a locally aggressive synovial proliferation that engenders progressive destruction of cartilage and bone. Two cases, a diffuse and a localized form, are reported. CASE REPORT: 1) A 9.9-year-old boy followed up for a popliteal cyst presented with chronic arthritis of the left knee. Aspiration yielded a bloody synovial fluid. MRI showed a heterogeneous synovial process with decreased signal in both T1- and T2-weighted images. The diagnosis of PVS was made on histology of an excisional biopsy. A complete open synovectomy was then performed. 2) A 13.8-year-old boy had a palpable mass on the internal side of the right patellofemoral joint. MRI showed a heterogenous mass with areas of hypointensity on all spin echo sequences corresponding to hemosiderin deposits suggestive of PVS. Surgical excision of a reddish-brown circumscribed lesion was performed. Diagnosis of PVS was made at surgery and confirmed by histologic examination. CONCLUSION: PVS diagnosis is frequently delayed due to nonspecific symptoms. Bloody fluid aspiration and MRI are valuable tools for early diagnosis. Treatment is surgical: extensive synovectomy for the diffuse form, excision of the lesion for the localized form.

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Adolescent Arthritis Child Diagnosis, Differential Humans Knee Joint Magnetic Resonance Imaging Male Synovitis, Pigmented Villonodular Case Reports English Abstract Journal Article

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D Rosenberg, R Kohler, E Chau, R Bouvier, J M Pouillaude, L David. 2001. [Pigmented villonodular synovitis. Diffuse and localized forms in children].. https://doi.org/10.1016/s0929-693x(00)00214-1

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