Chiari type III malformation.

Massimo Caldarelli; Giancarla Rea; Rafael Cincu; Concezio Di Rocco

doi:10.1007/s00381-002-0579-y

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PubMed · 12042918

Chiari type III malformation.

Massimo Caldarelli·Giancarla Rea·Rafael Cincu·Concezio Di Rocco

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Abstract

BACKGROUND: Chiari type III is the rarest of the Chiari malformations, and it is usually associated with a dismal prognosis in terms of early death or severe disability in long-term survivors. Surgical treatment usually consists of primary closure of the occipital/cervical encephalocele, followed by delayed CSF shunting for the associated hydrocephalus. METHODS: In our case, we introduced a technical variant consisting in primary external drainage from the malformative sac, followed by closure of the encephalocele and, eventually, by CSF shunting.

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Massimo Caldarelli, Giancarla Rea, Rafael Cincu, Concezio Di Rocco. 2002-04-18. Chiari type III malformation.. https://doi.org/10.1007/s00381-002-0579-y

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