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[Macronodular adrenal hyperplasia: a case report].

A Benchekroun·Y Nouini·M Zannoud·H el Kasmaoui·L Benslimane·M Faik
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Abstract

This case report describes a 53-year old man with Cushing's syndrome due to Adrenocorticotropic Hormone (ACTH) independent bilateral adrenocortical macronodular hyperplasia (AIMAH). His plasma cortisol showed no diurnal rhythm and was unsuppressable by high-dose dexamethasone. Plasma ACTH was undetectable and did not respond to corticotrophin-releasing hormone. The aetiology of this rare disease remains uncertain. The treatment is based on bilateral adrenalectomy.

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Adrenal Gland DiseasesAdrenalectomyAdrenocorticotropic HormoneCushing SyndromeFemaleHumansHydrocortisoneHyperplasiaMiddle AgedTreatment OutcomeCase ReportsEnglish AbstractJournal Article

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A Benchekroun, Y Nouini, M Zannoud, H el Kasmaoui, L Benslimane, M Faik. 2003. [Macronodular adrenal hyperplasia: a case report].. https://doi.org/10.1016/s0003-4401(03)00008-1

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