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PubMed · 14561599

Mesectodermal leiomyosarcoma of the ciliary body.

Sun-Won Park·Hyung-Jin Kim·Hee-Seung Chin·Kee-Sun Tae·Jee-Young Han
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Abstract

We report a case of low-grade mesectodermal leiomyosarcoma of the ciliary body, an extremely rare tumor of neural crest origin, occurring in a 12-year-old boy. MR imaging showed a well-marginated, ovoid soft tissue mass at the right temporal ciliary body, accompanied by total retinal detachment. The mass was slightly hyperintense relative to contralateral vitreous on T1-weighted images and markedly hypointense on T2-weighted images and enhanced very well. Initial biopsy of the mass suggested a peripheral nerve sheath tumor. The mass grew rapidly after biopsy, and enucleation was performed. The final diagnosis based on histology and immunohistochemistry was a low-grade mesectodermal leiomyosarcoma. To our knowledge, this is the first reported case of a malignant form of mesectodermal leiomyoma of the ciliary body.

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ChildCiliary BodyDiagnosis, DifferentialHumansLeiomyosarcomaMagnetic Resonance ImagingMaleUveal NeoplasmsCase ReportsJournal Article

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Sun-Won Park, Hyung-Jin Kim, Hee-Seung Chin, Kee-Sun Tae, Jee-Young Han. 2003. Mesectodermal leiomyosarcoma of the ciliary body.. https://pubmed.ncbi.nlm.nih.gov/14561599/

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