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PubMed · 1485110

[Disseminated complex vascular malformations].

O Enjolras
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Abstract

Diffuse complex vascular malformations are sporadic or hereditary. They usually concern one type of vessel: capillary, venous or arterial (with AV fistula). They involve skin, mucosal membranes and internal organs. They lead to a rich and heterogeneous symptomatology, depending on the lesional localizations. Five out of them are described: cutis marmorata, Rendu Osler disease, Bean syndrome, Maffucci syndrome, and Proteus syndrome.

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Abnormalities, MultipleArteriovenous MalformationsEnchondromatosisHumansNevusProteus SyndromeTelangiectasia, Hereditary HemorrhagicTelangiectasisEnglish AbstractJournal Article

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O Enjolras. 1992-10-15. [Disseminated complex vascular malformations].. https://pubmed.ncbi.nlm.nih.gov/1485110/

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