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[Peripheral neuroblastic tumors: anatomo pathological classification].

M Peuchmaur
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Abstract

Peripheral Neuroblastic Tumors are classified according to the recommendations of the INPC into four categories and their subtypes: 1/Neuroblastoma stroma poor, undifferentiated, poorly differentiated, and differentiating, 2/ganglioneuroblastoma stroma composite, nodular, 3/ganglioneuroblastoma stroma composite, intermixed and 4/ganglioneuromas stroma dominant, maturing and mature. The classification is based on age and morphologic features of PNT, including the differentiation grade of the neuroblasts and the mitosis-karyorrhexis index. Histopathological classification has prognostic impact in predicting overall and event-free survival allowing the categorisation of PNT into two groups: favorable subset and unfavorable subset.

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GanglioneuroblastomaGanglioneuromaHumansNeuroblastomaPeripheral Nervous System NeoplasmsEnglish AbstractJournal ArticleResearch Support, Non-U.S. Gov'tReview

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M Peuchmaur. 2004. [Peripheral neuroblastic tumors: anatomo pathological classification].. https://doi.org/10.1016/s0242-6498(04)94018-7

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