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PubMed · 16943479

Extra-axial chordoma.

A C J van Akkooi·A N van Geel·J H J M Bessems·M A den Bakker
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Abstract

A chordoma which occurs as a primary tumour outside the axial skeleton is known as an extra-axial chordoma, parachordoma or chordoma periphericum. It is extremely rare and therefore survival, recurrence and the rates of metastasis are not known. Whilst few recurrences have been described, the extra-axial chordoma has the potential for late recurrence at up to 12 years. Metastases are even less frequent. We report the case of a 56-year-old woman who developed an extra-axial chordoma of the right thoracic wall in close relationship with the tenth rib. The tumour was completely removed and the prognosis is excellent.

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ChordomaFemaleHumansMiddle AgedThoracic NeoplasmsThoracic WallTreatment OutcomeCase ReportsJournal Article

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BibTeXRIS

A C J van Akkooi, A N van Geel, J H J M Bessems, M A den Bakker. 2006. Extra-axial chordoma.. https://doi.org/10.1302/0301-620x.88b9.17873

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