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PubMed · 17202607

Polyglandular autoimmune syndrome-type I.

Rajesh R Joshi·Sudha Rao·S S Prabhu
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Abstract

Polyglandular autoimmune syndrome type I is a rare disorder characterized by mucocutaneous candidiasis (MC), hypoparathyroidism (HP) and adrenal insufficiency , requiring regular follow up as the components of the syndrome appear at different age groups. We report a six and half year boy having this syndrome and presenting with MC, HP and ectodermal dystrophy.

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Candidiasis, Chronic MucocutaneousChildEctodermal DysplasiaHumansHypoparathyroidismMalePolyendocrinopathies, AutoimmunePrognosisCase ReportsJournal Article

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Rajesh R Joshi, Sudha Rao, S S Prabhu. 2006. Polyglandular autoimmune syndrome-type I.. https://pubmed.ncbi.nlm.nih.gov/17202607/

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