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SLE-like and sicca symptoms in late component (C9) complement deficiency.

M Sugimoto·M Nishikai·A Sato·Y Suzuki·M Nihei·J Uchida·N Mimura
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Abstract

Hereditary deficiencies in early and late complement components are well known to predispose to SLE-like syndromes or recurrent infection. Hitherto reported C9 deficient cases have usually been healthy subjects, however, and it is not considered that C9 deficiency is associated with any specific disease. We describe a completely C9 deficient patient with possible Sjögren's syndrome and discuss the relationship.

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Autoimmune DiseasesComplement C9FemaleHumansMiddle AgedPedigreeSjogren's SyndromeCase ReportsJournal Article

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M Sugimoto, M Nishikai, A Sato, Y Suzuki, M Nihei, J Uchida, N Mimura. 1987. SLE-like and sicca symptoms in late component (C9) complement deficiency.. https://doi.org/10.1136/ard.46.2.153

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