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PubMed · 4020785

Müllerian dysgenesis.

R E Varner·J B Younger·R E Blackwell
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Abstract

The multifaceted syndrome of müllerian dysgenesis appears to represent a defect in mesodermal organization and is often associated with renal and skeletal anomalies. This report discusses the embryology, multifactorial etiology, clinical presentation and management of the syndrome from a historical standpoint and details our experience with 35 affected patients. Both Frank dilatation and McIndoe vaginoplasty appear to be acceptable means of therapy. The therapeutic success depends to a large extent on the psychosocial adaptation of the patient.

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Abnormalities, MultipleAdolescentAdultChildChild, PreschoolDilatationFemaleHumansMullerian DuctsSex Chromosome AberrationsUterusVaginaJournal Article

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R E Varner, J B Younger, R E Blackwell. 1985. Müllerian dysgenesis.. https://pubmed.ncbi.nlm.nih.gov/4020785/

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