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PubMed · 5059566

Galactose utilization in galactosemia.

J C Petricciani·M K Binder·C R Merril·M R Geier
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Abstract

Cultures of human galactosemic fibroblasts without detectable transferase activity were able to convert [1-(14)C]galactose to (14)CO(2) to the same extent as normal cells, but did so at a significantly slower rate. The utilization of galactose in both normal and galactosemic cells was strongly inhibited by glucose at physiologic concentrations.

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Carbon DioxideCarbon IsotopesCells, CulturedFibroblastsGalactoseGalactosemiasGlucoseHumansJournal Article

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J C Petricciani, M K Binder, C R Merril, M R Geier. 1972-03-24. Galactose utilization in galactosemia.. https://doi.org/10.1126/science.175.4028.1368

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