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Visual system abnormalities in adrenomyeloneuropathy.

P W Kaplan·B Kruse·R J Tusa·J Shankroff·J Rignani·H W Moser
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Abstract

We studied the visual system in 59 men with adrenomyeloneuropathy. Pattern-reversal visual evoked potentials, magnetic resonance imaging, and clinical examination revealed that visual pathways are affected in 63% of patients, involving the optic discs, optic nerves, lateral geniculate bodies, optic radiations, and parietooccipital cortex. This indicates both primary demyelination of the optic nerves and discs, and more diffuse involvement of postchiasmal structures.

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AdrenoleukodystrophyAdultEvoked Potentials, VisualHumansMagnetic Resonance ImagingMaleMiddle AgedPhotic StimulationVision DisordersJournal ArticleResearch Support, U.S. Gov't, P.H.S.

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P W Kaplan, B Kruse, R J Tusa, J Shankroff, J Rignani, H W Moser. 1995. Visual system abnormalities in adrenomyeloneuropathy.. https://doi.org/10.1002/ana.410370419

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