[Caroli's syndrome: a variable entity].

M D Espinosa Aguilar; M López de Hierro Ruiz; L M Pinel Julián; A González Galilea; J F Suárez Crespo; M Ruiz-Cabello; R Martín-Vivaldi

PubMed · 7848699

[Caroli's syndrome: a variable entity].

M D Espinosa Aguilar·M López de Hierro Ruiz·L M Pinel Julián·A González Galilea·J F Suárez Crespo·M Ruiz-Cabello·R Martín-Vivaldi

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Abstract

We present the case of a 56 year old woman with Caroli's disease associated to congenital liver fibrosis, renal nephrocalcinosis and cutaneous vasculitis of the legs. Clinical signs of portal hypertension were treated by a shunt technique. After an asymptomatic period, the patient suffers now from crisis of angiocholitis.

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Caroli Disease Female Humans Middle Aged Case Reports English Abstract Journal Article

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M D Espinosa Aguilar, M López de Hierro Ruiz, L M Pinel Julián, A González Galilea, J F Suárez Crespo, M Ruiz-Cabello, R Martín-Vivaldi. 1994. [Caroli's syndrome: a variable entity].. https://pubmed.ncbi.nlm.nih.gov/7848699/

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