Split notochord syndrome: case report.

N Razack; L K Page

doi:10.1227/00006123-199511000-00023

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Split notochord syndrome: case report.

N Razack·L K Page

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Abstract

Split notochord syndrome includes a cleft of the vertebral column associated with malformation of the central nervous system. Fourteen cases involving the lumbosacral spine have been reported in the literature. We report on a female neonate who had intact function of her lower extremities, a posterior midline lumbar defect bounded by two complete spinal canals that contained two spinal cords. A meningocele, a large bowel fistula, and a mature teratoma protruded through the cleft. The baby is doing well after repair of the anomaly and placement of a ventriculoperitoneal shunt.

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Arnold-Chiari Malformation Female Follow-Up Studies Humans Infant, Newborn Lumbar Vertebrae Magnetic Resonance Imaging Meningocele Notochord Spinal Neoplasms Teratoma Ventriculoperitoneal Shunt Case Reports Journal Article

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N Razack, L K Page. 1995. Split notochord syndrome: case report.. https://doi.org/10.1227/00006123-199511000-00023

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