Ewing's sarcoma and peripheral primitive neuroectodermal tumor: an interim report.

J G Batsakis; B Mackay; A K el-Naggar

doi:10.1177/000348949610501014

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Ewing's sarcoma and peripheral primitive neuroectodermal tumor: an interim report.

J G Batsakis·B Mackay·A K el-Naggar

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Abstract

The primitive neuroectoderm and its progeny seemingly give rise to an ever-increasing number of clinicopathologic entities. Ewing's sarcoma and peripheral primitive neuroectodermal tumor have recently been united by relatively unique antigens expressed by the MIC-2 gene, commonly coexpressed neural markers, and cytogenetic and molecular genetic abnormalities. Because of these factors, the current thinking is that Ewing's sarcoma and the peripheral primitive neuroectodermal tumor are parts of a phenotypic spectrum. We present an "interim report" on this group of neoplasms, emphasizing their presentation in the head and neck.

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Female Head and Neck Neoplasms Humans Male Neuroectodermal Tumors, Primitive Sarcoma, Ewing Journal Article Review

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J G Batsakis, B Mackay, A K el-Naggar. 1996. Ewing's sarcoma and peripheral primitive neuroectodermal tumor: an interim report.. https://doi.org/10.1177/000348949610501014

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