Small aortic root in neonates.

Abstract

Small aortic root in neonates and infants is usually associated with unicommissural aortic valve, namely the presence of only one leaflet with eccentrically located commissure. This condition implies aortic stenosis because of: (i) a small aortic ring diameter; (ii) an intrinsically stenotic unicommissural orifice; and (iii) a dysplastic leaflet with myxoid nodular excrescences. The frequent association with hypoplastic left ventricle, fibroelastosis, dysplastic mitral valve and aortic arch obstructions prohibits a biventricular repair.