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PubMed · 9725451

Pathologic substrates for 1 1/2 ventricular repair.

Abstract

BACKGROUND: The concept of "one and a half ventricular repair" relates to situations where one ventricle is capable of pumping one half of the circulation while the other ventricle is deemed inadequate and requires off-loading by means of a shunt. The inadequate ventricle is usually assigned the role of pumping the pulmonary circulation. The majority of hearts potentially amenable to this repair will have one large ventricle associated with a smaller and more-or-less rudimentary ventricle. METHODS: In this review, we focused on hearts in which the morphologically left ventricle will continue to support the systemic circulation. RESULTS: Among the hearts with univentricular atrioventricular connections, a few cases of classic tricuspid atresia and cases of double-inlet left ventricle coexisting with concordant ventriculoarterial connections would be suitable for incorporating the right ventricle into the pulmonary circulation. This procedure may be feasible in some cases of straddling and overriding tricuspid valve. Hearts with pulmonary atresia and intact ventricular septum display a wide range of sizes of the right ventricular cavity. Although biventricular repair is an option for those with good-sized cavities, patients with hypoplastic right ventricles may be candidates for one and a half ventricular repair. CONCLUSIONS: For the lesions reviewed, and many others, one and a half ventricular repair can be an option.

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BibTeXRIS

R H Anderson, S Y Ho. 1998. Pathologic substrates for 1 1/2 ventricular repair.. https://doi.org/10.1016/s0003-4975(98)00575-x

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Morphologic features of the uniatrial but biventricular atrioventricular connection.

OBJECTIVES: Hearts with an absent atrioventricular connection and a straddling of the solitary atrioventricular valve are rare but significant lesions. They are suitable only for Fontan-like palliation, in which atrioventricular valvar abnormalities play a significant role in determining the outcome. We studied the segmental arrangements in such lesions and clarified the valvar morphology, particularly its surgical implications. METHODS: We made a macroscopic review of all specimens with an absent atrioventricular connection and a straddling atrioventricular valve that were held in the collections of 3 institutes. We included only those specimens with the straddling valve supported exclusively by either the right-sided or left-sided atrioventricular junction and excluded those with a common atrioventricular junction. RESULTS: We found 11 hearts with an absent right atrioventricular connection and a straddling left atrioventricular valve, and 3 with an absent left atrioventricular connection and a straddling right atrioventricular valve. Most had right-hand ventricular topology and discordant ventriculoarterial connections. We found multiple valvar abnormalities, including dysplastic leaflets, short cords, abnormal attachments, and abnormal papillary muscles. The most consistent features were a line of maximal coaptation between the bridging leaflets always perpendicular to the plane of the ventricular septum and a free-floating bridging anterosuperior leaflet. CONCLUSIONS: Straddling of a solitary atrioventricular valve with an absent atrioventricular connection produces a uniatrial but biventricular connection. In this setting, the valve guarding the abnormal solitary atrioventricular junction cannot be classified morphologically as mitral or tricuspid. The markedly variable valvar morphology likely makes these valves prone to insufficiency in the long term.

Heart Defects, Congenital↗