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Results for “CLEIDOCRANIAL DYSOSTOSIS”

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PubMed1987

The surgical and orthodontic management of unerupted teeth in cleidocranial dysostosis.

A common feature of patients with cleidocranial dysostosis is delayed shedding of deciduous teeth and failure of eruption of the permanent dentition. This article describes a method whereby orthodontic forces may be applied to these unerupted permanent teeth to move them into a satisfactory functional and aesthetic position with good periodontal support whilst maintaining their vitality. This method of treatment avoids the need for overdentures or other prosthetic aids which have often been used in the past.

Adolescent↗
PubMed1976

[Contribution to the clinical picture and hereditary nature of cleidocranial dysostosis].

In the light of 5 cases and of the relevant literature, the author discusses the clinical picture, inheritance and treatment of cleidocranial dysostosis. It is stated that, though the manifestations of cleidocranial dysostosis are varied, this disease is in most cases characterized by a sagittal frontal sulcus with partially closed frontal fontanel and hypertelorism. The author pleady for the regular medical supervision of these patients.

Abnormalities, Multiple↗
PubMed1987

Cleidocranial dysostosis and syringomyelia. Review of the literature and case report.

A 34-year-old woman with congenital cleidocranial dysostosis had scoliosis diagnosed at age 13. The scoliosis was treated during adolescence with spinal orthoses but continued to progress after skeletal maturation. She was diagnosed as having syringomyelia at age 34. The possibility of syringomyelia should be considered in patients with cleidocranial dysostosis, especially those with neurologic symptoms, scoliosis not responding to conservative therapy, or progressive scoliosis after skeletal maturation. Although only two previous patients have been reported in the literature, the condition undiagnosed could be a more common problem than generally supposed.

Adult↗
PubMed2001

Cleidocranial dysostosis and the unity of the Homeric epics: an essay.

Numerous years ago, in this journal, Beasley diagnosed the character Thersites from Homer's Iliad with cleidocranial dysostosis. Additional evidence from the text is presented to support a diagnosis of cleidocranial dysostosis, and it is pointed out that this diagnosis may have implications in studying the question whether the two Homeric epics (the Iliad and the Odyssey) were composed by the same author.

Cleidocranial Dysplasia↗
PubMed1997

Cleidocranial dysostosis: report of a case.

This case of cleidocranial dysostosis showed nearly 40 accessory teeth and the unerupted teeth on radiological examinations. Other diagnostic procedures found hypoplasia in maxillary and zygomatic bones, deep palate, open fontanel and open sutures, the collapse of sagittal suture, and aplasia of the clavicle. There were some abnormalities of the fingers. Under general anesthesia eleven supernumerary teeth in the mandible and eight in the maxilla were surgically extracted. Upper and lower removable acrylic appliances were fabricated.

Child↗
PubMed1989

[A study of genetic influence on the cranial base variations in cases with cleidocranial dysostosis].

The purpose of the present study was an investigation of the hereditary influence on the shape and size of the cranial base in cases with cleidocranial dysostosis, in an attempt to contribute to an improved understanding of the syndrome. The sample consisted of 32 patients with cleidocranial dysostosis. Out of these 32 cases, 21 were affected members of 7 families and 11 sporadic cases. Quantitative and qualitative types of study were performed on the lateral skull radiographs. The first part of study involved a metric analysis of the angle NSBa and lengths of the anterior (N-S) and posterior (S-Ba) parts of the cranial base as well as the total length of the cranial base (N-Ba). The second part of this study involved a superimposition of the cranial base as well as its parts (pituitary fossa, anterior and posterior clinoid processus, dorsum sellae and the part of clivus facing the endocranium) in both the family and sporadic cases in order to assess the degree of similarity between them. In the first part of study a comparison was made between sample with syndrome and a control sample consisting of normal cases of adequate sex and age. Significance of differences between the samples was calculated by using t test. It was found that the sample with syndrome demonstrated significantly lower mean values of N-S, S-Ba and N-Ba dimensions. The mean value of NSBa angle was lower in the sample with syndrome but there was no significant difference. Following this, cases with the syndrome were divided in two groups: familial and sporadic.(ABSTRACT TRUNCATED AT 250 WORDS)

Cephalometry↗
PubMed1998

Cleidocranial dysostosis--a case report and review of the literature.

Cleidocranial dysostosis is a generalised dysplasia of bone and teeth with predominantly autosomal dominant inheritance. A new case referred to the Paediatric Department at the British Military Hospital, Rinteln is reported and a review of the literature discussed.

Child, Preschool↗
PubMed1978

Prosthodontic therapy for cleidocranial dysostosis: report of case.

Objectives of treatment of the oral manifestations of cleidocranial dysostosis should include restoring the vertical dimension of occlusion, building out the maxilla, establishing of functional occlusion, improving appearance and phonation, and improving the patient's mental well-being.

Adolescent↗
PubMed1978

Cleidocranial dysostosis: report of case.

In the treatment of oral problems of patients with cleidocranial dysostosis, the multidisciplinary approach should be considered. The collective abilities of the oral surgeon, the prosthodontist, and the orthodontist should be utilized to determine the most effective treatment.

Adult↗
PubMed2001

Histological and analytical studies of a tooth in a patient with cleidocranial dysostosis.

A histopathological and analytical study of a permanent tooth from a patient with cleidocranial dysostosis (CCD) was performed. The patient was a 47-year-old woman, who had 10 erupted permanent teeth and 2 partially erupted and 19 completely impacted teeth, including supernumerary teeth. The erupted right upper premolar was extracted and observed using a light microscope and an electron probe X-ray microanalyzer (EPMA). Findings showed enamel hypoplasia, predominantly irregular globular dentin and Tomes' granular layer, and a complete lack of cellular cementum in the ground section. The incremental von Ebner and counter Owen lines were obscure. Comparative quantitative analysis using the EPMA showed that the quantities of calcium and phosphate were lower in the enamel and dentin than those of the control sample.

Bicuspid↗