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At least 55 records · Page 3Linked to original sources
PubMed1991

[A successful case of double outlet right ventricle accompanied with complete endocardial cushion defect].

Surgical correction of a case of double outlet right ventricle accompanied with complete endocardial cushion defect was completed successfully. No other complicated anomaly existed in this case. Correction was done by using two patch method. The patch for VSD was designed to be comma-like shape. For ensuring the left ventricular out tract, the patch was sutured with bulging at the circumference of the aortic orifice and the suture line of the patch with atrio-ventricular valve was deviated to the right. There was no stenosis in the left ventricular out tract and tricuspid valve.

Child, Preschool↗
PubMed1985

Complete endocardial cushion defect: the late result of repair using the single-patch technique.

Twenty-two patients have been followed for between 1 and 105 months after repair of a complete endocardial cushion defect. The mean period of follow-up is 3.5 years. The single-patch technique was used in every patient. The mitral valve was repaired with buttressed sutures in those seen more recently. The mean age at the time of operation was 15 months. Early in this experience, 4 patients had severe mitral valve incompetence after an initially satisfactory repair. In none of those patients had the mitral valve been repaired with pledgeted sutures. Two of those patients survived reoperation, and 2 died before a second operation could be performed. Every mitral valve is now repaired with pledgeted sutures, and there have been no failures of the mitral valve reconstruction. Each patient has been followed by the same pediatric cardiologist every 6 to 12 months after operation. The vast majority (17 of 20) are asymptomatic. Twelve have no mitral valve incompetence, and the remainder have only trivial or mild incompetence. Clinically, the pulmonary artery hypertension has resolved in 19 of 20 patients. Each patient remains in normal sinus rhythm. The long-term results following repair of complete endocardial cushion defect with the single-patch technique are excellent, but pledgeted sutures should be used in the mitral valve repair to insure its integrity.

Endocardial Cushion Defects↗
PubMedDate not supplied

[Electro-vectorcardiographic behavior of right bundle branch block in endocardial cushion defects. Its probable relation to the so-called left anterior fascicular hemiblock].

We have investigated the possible ECG signs of incomplete Left Anterior Hemiblock (LAH). As an experimental model we chose the endocardial cushion defect, which is proved to have a ventricular activation correspondent to different degrees of LAH due to the particular disposition of the AV node and the His bundle. The VCG of 50 patients with endocardial cushion defect were divided into 5 groups according to the entity of the left and superior deviation of the maximum left vector. Comparison with the ECG signs shows that: a) minimal degrees of LAH occur with simple counterclockwise rotation of the frontal loop without a significant left axis deviation; b) there is no linear correlation between the importance of the left axis deviation and the signs of left ventricular activation asincronism. We conclude that, with the exception of this particular congenital heart disease, minimal LAH degrees can only be suspected on the basis of a counterclockwise VCG frontal loop, because the ECG diagnosis is possible only when the left axis deviation becomes important.

Adolescent↗
PubMed1982

Subacute bacterial endocarditis and complete endocardial cushion defect.

Subacute bacterial endocarditis involving the common atrioventricular (AV) valve is a rare complication of complete endocardial cushion defect. This report describes our experience with an 18-year-old patient who was seen with this problem. Diagnosis was established by two-dimensional echocardiography. The operative findings and technique of repair are described. We believe this to be among the first successful reports of complete repair of active endocarditis involving the common AV valve in this congenital anomaly.

Adolescent↗
PubMed1996

[Surgical treatment of double-orifice mitral valve associated with incomplete-type endocardial cushion defect].

We report surgical treatment of double-orifice mitral valve (DOMV) associated with incomplete-type endocardial cushion defect. All three cases had "central type DOMV classified by Cascos" with bridging tissue between two mitral orifices. We closed mitral cleft in the two cases with moderate mitral regurgitation, although we left the bridging tissue. It is thought to be beneficial to leave the bridging tissue undivided to avoid postoperative mitral regurgitation in such cases.

Adult↗
PubMed1995

[Surgical treatment of incomplete endocardial cushion defect in adult patients].

Seven adult patients (> or = 40 years old) and six pediatric patients with incomplete endocardial cushion defect (ECD) underwent corrective surgery in our institution. Preoperative catheterization study showed that the left-to-right shunting rate and the pulmonary-to-systemic flow ratio were greater in adult patients than those in pediatric patients, but systolic pulmonary arterial pressure was not high and similar in the two groups. The degree of mitral regurgitation by left ventriculography was mild or moderate in both groups. However, in adult patients, a variety of arrhythmias were observed. Postoperatively, NYHA grades and arrhythmia improved markedly in the adult patients. Surgical correction for ECD is recommended even in adult patients before aggravation of cardiac failure and arrhythmia.

Adult↗
PubMedDate not supplied

[Endocardial cushion defects in situs solitus and in asplenic and polysplenic syndromes, Anatomoembryological correlations].

The endocardial cushion defects were studied in hearts belonging to situs solitus and in the asplenia and polysplenia syndroms. WE propose that these defects must be classified by identifying persistent developmental stages. Such classification would content the anatomical varieties seen in the asplenia and polysplenia syndroms. The embryological bases are discussed.

Endocardium↗
PubMed1992

[An autopsy case of endocardial cushion defect (ECD) in an 82-year-old female].

In an 82-year-old female case of endocardial cushion defect (ECD), a systolic regurgitant murmur was heard at the apex, and her ECG showed atrial fibrillation without right bundle branch block or left axis deviation. An echocardiogram demonstrated atrial septal defect (ASD) and a cleft of the anterior mitral leaflet with calcification. She died of refractory congestive heart failure. Autopsy revealed ECD (intermediate type) with mitral and tricuspid cleft, and ASD (ostium primum type, 2.0 x 1.0 cm in diameter). In addition, mitral ring calcification and calcification of the cleft mitral valve was disclosed, causing mitral stenosis in addition to mitral regurgitation due to the cleft mitral valve. This was the second oldest Japanese autopsy case of ECD. We concluded that echocardiographic examinations, including color flow imaging, in aged patients with heart murmur are necessary to confirm the diagnosis of congenital heart disease in the aged.

Aged↗
PubMed1976

Endocardial cushion defects: an anatomical study of 54 specimens.

An anatomical study of 54 specimens with endocardial cushion defect is described. The material was divided into two groups, according to the morphology and attachments of the anterior component of the anteroseptal mitral leaflet. We suggest that there is no divided or undivided anterior common leaflet. There are always two anterior leaflets, a mitral and a tricuspid one, separated by a commissure; depending on the degree of straddling of the mitral component over the interventricular septum, this will protrude into the interventricular septum or into the anterior papillary muscle of the right ventricle. Thus, the commissure separating the mitral and the tricuspid components will lie over the interventricular septum or will be quite separate in the right ventricle. In the latter case the straddling mitral component gives the false appearance of an undivided anterior common leaflet. The septal tricuspid leaflet was found to be underdeveloped or absent but we were not able to find any clefts or divisions in it. We suggest that this leaflet derives solely from the division of the posteroinferior endocardial cushion into two halves, right and left. The left half later becomes the posterior component of the normal anteroseptal mitral leaflet. Associated anamalies are also reviewed.

Ductus Arteriosus, Patent↗
PubMed1982

[Endocardial cushion defect without ostium primum atrial septal defect associated with tetralogy of Fallot (author's transl)].

A case of endocardial cushion defect without ostium primum atrial septal defect associated with tetralogy of Fallot is presented. The echocardiogram is specially interesting showing two atrioventricular valves recorded simultaneously without an intervening ventricular septum, mitral continuity with the posterior semilunar valve and impossibility of recording the anterior semilunar valve. Findings similar to those of single ventricle with pulmonary stenosis. The anatomopathological findings and their possible embryonic basis are analyzed.

Down Syndrome↗
PubMed1975

Echocardiography in endocardial cushion defects: a preoperative and postoperative study.

Echocardiographic studies were performed on 14 patients with endocardial cushion defects of different anatomic varieties. Four patients were studied again after operation. Patients with partial atrioventricular canal (PAVC) showed multiple systolic echoes on mitral valve echogram, with significant mitral-septal apposition in diastole. The left ventricular outflow (LVO) appeared significantly narrowed. The septal motions were paradoxic. After corrective operation, an increase in the width of the LVO was noted and mitral-septal apposition appeared to be less pronounced. Multiple systolic echoes, however, reappeared and persisted. The echocardiograms in patients with complete atrioventricular canal (CAVC) were characterized by wide excursion of an apparent single atrioventricular valve. The echoes of the mitral component of the common anterior leaflet moved anteriorly into the right ventricular cavity and overshadowed the tricuspid component in diastole. In addition, patients with CAVC and divided and medially attached common anterior leaflets had solitary mitral and tricuspid echograms. This feature differentiates this group of patients from those patients with CAVC with undivided freefloating common anterior leaflet.

Adolescent↗
PubMed1999

[Severe hypoxia due to persistent left supra vena cava draining to the left atrium after weaning from cardiopulmonary bypass in a patient with endocardial cushion defect].

We report a case of severe hypoxia after weaning from cardiopulmonary bypass in a ten-month-old patient with endocardial cushion defect. The severe hypoxia was improved abruptly when the persistent left supra vena cava (PLSVC) was ligated. The hypoxia, therefore, was considered to be caused by venous blood which was directly drained into the left atrium through the PLSVC. In cases with large right-to-left shunt which is difficult to explain only by intracardiac shunt, attention must be paid to existence of PLSVC directly draining into the left atrium.

Anesthesia, General↗
PubMed1976

Echocardiographic analysis of intracardiac anatomy in endocardial cushion defect.

A standard echocardiographic technique was proposed for an analysis of the intracardiac anatomy of endocardial cushion defect (ECD). It consisted of two beam directions, mitral and tricuspid, and two M-mode scans, between the mitral and tricuspid valves and between the mitral and aortic valves. Using this technique, echocardiographic studies were performed on 13 patients with ECD, including 10 patients with the incomplete form and three patients with the free-floating form. In patients with the incomplete form, an M-mode scan between the mitral and tricuspid valves showed the specific features of the interaction between the mitral valve, the interventricular septum, and the tricuspid valve, termed the "mitral-interventricular septal-tricuspid (MVT) connection." The systolic multiple echoes and the diastolic echoes of the so-called posterior leaflet of the mitral valve were constant findings in the mitral direction. The tricuspid valve, although less continuous, was recorded simultaneously with the mitral valve in the same direction. Ateriorly displacement of the anterior mitral leaflet was shown on an M-mode scan between the mitral and aortic valves, giving an echocardiographic representation of the angiocardiographic "goose-neck" sign. Evidence showing the presence of right ventricular volume overload was also found. In patients with the free-floating form, an anterior common A-V valve with a large excursion was recorded on an M-mode scan between the mitral and tricuspid valves. The valve was located posterior to the interventricular septum in the mitral direction and anterior to the septum in the tricuspid direction. There was no finding to show the interaction between the valve and the septum. The posterior common A-V valve was registered only in the mitral direction. Our technique made it possible to diagnose ECD, using a noninvasive echocardiographic method, and discriminate the free-floating form from other forms of ECD.

Adolescent↗
PubMed2003

Catheter ablation for a right anteroseptal accessory pathway in a patient with an endocardial cushion defect.

We report a radiofrequency catheter ablation for atrioventricular reentrant tachycardia in a patient with a right anteroseptal accessory pathway complicating an endocardial cushion defect. His bundle potential was recorded 20 mm posterior to the accessory pathway. In the presence of associated congenital heart disease, it is very important to understand the anatomy of the conduction system prior to radiofrequency catheter ablation.

Adolescent↗
PubMed1997

[Surgical correction of an incomplete endocardial cushion defect in a 66-year-old male with the remarkable pulmonary hypertension].

A surgical case of a 66-year-old male with an endocardial cushion defect (ECD) is reported. He had preoperative pulmonary hypertension (80/25 mmHg, Pp/Ps 0.61), hypoxia (63.7 mmHg) and decreased creatinin clearance (45.7 ml/min). Respiratory condition was New York Heart Association's (NYHA's) grade III. Angiocardiography showed a typical gooseneck deformity associated with mitral and tricuspid valve regurgitations with the cleft (Seller's grade II and III). As surgical correction, direct suture of the cleft in an anterior leaflet with mitral annuloplasty, patch closure of the ostium primum defect with Xenomedical patch and tricuspid annuloplasty were performed. Postoperative data were restored to NYHA grade I. decreased pulmonary artery pressure (43/21 mmHg) and resistances (Pp/Ps 0.36). The only three surgical treatments of an incomplete ECD were reviewed in over 65-year-old patients in Japan included one perioperative death. Although we suggest it should be actively taken surgical repair even in elderly patients with pulmonary hypertension.

Aged↗