Vaginal agenesis associated with anhidrotic ectodermal dysplasia.
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A case of a 10-year old boy with anhidrotic ectodermal dyspasia is reported. The classic triad has been established--hypodontia, hypotrichosis and anhidrosis, confirmed by biopsy. The patient's genealogy was studied, revealing inheritance by C-chromosome. The early treatment results in functional, aesthetic and psychological effect. The prostheses should periodicaly be changed so as to guarantee the proper development of the jaws.