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Results for “Truncus Arteriosus, Persistent”

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At least 595 records · Page 33Linked to original sources
PubMed1990

[Color-coded Doppler sonography of the kidney blood vessels in childhood. II. Pathological findings].

Pathologic flow profiles in renal arteries can be found in cardiovascular and renovascular disease. Obstructions of the left hart (aortic stenosis, hypoplastic left heart syndrome, coarctation of the aorta) cause diminished flow with low peak systolic velocities. In renal arteries of infants with leakage of the aortic "Windkessel" (persistent ductus arteriosus, truncus arteriosus communis etc.) a low diastolic amplitude can be found. Significant left-to-right shunts can lead to a diminished or even retrograde diastolic flow. In renal artery stenosis a high velocity jet with spectral broadening can be found in the region of the stenosis. Distal to the stenosis low blood flow velocities can be shown. In renal vein thrombosis the obstruction of the peripheral vessels cause a missing or even negative diastolic flow in the renal arteries, whereas venous blood flow is diminished or even missing. Kidney diseases with swelling of the organ (acute rejection of a transplanted kidney) can cause diminished, missing or even retrograde diastolic flow in the renal arteries dependent on the severity of the edema. These alterations can be used for the early diagnosis of acute rejection which offers the opportunity for early and efficient therapeutic management.

Cardiovascular Diseases↗
PubMed1990

[Successful correction of truncal valve regurgitation and conduit obstruction after previous Rastelli operation for truncus arteriosus (type I)].

A 9-year-old boy had a successful surgical correction of truncal valve regurgitation and obstruction of extracardiac conduit which ensued previous Rastelli operation. He underwent Rastelli operation at the age of 10 months with the diagnosis of truncus arteriosus (Collet & Edwards Type I). At the age of 8 years, he was admitted because of slow weight gain and cardiomegaly (CTR 64%). Cardiac catheterization showed elevated RV pressure, increased pressure gradient across the conduit and severe truncal valve regurgitation. The extracardiac conduit was replaced with a 22 mm Hancock valved conduit and the truncal valve with 23 mm St. Jude Medical aortic valve. Postoperative catheterization revealed a normal RV pressure, only slight pressure gradient across the conduit and no truncal valve regurgitation. He is doing quite well 2 years after the operation.

Blood Vessel Prosthesis↗
PubMed1989

[Asymptomatic common truncus arteriosus in a 25-year-old patient with paroxysmal tachycardia and truncal valve insufficiency].

We present an adult patient (25-years old), free of symptoms with a congenital heart disease very infrequent and survival to adulthood is exceptional, the truncus arteriosus. Who entered to the Emergency Care Unit because of paroxysmal tachycardia. We describe the case with special reference to echocardiographic findings and we detached the rarity of this congenital heart disease in adulthood.

Adult↗
PubMed1989

[Truncus arteriosus: an autosomal recessive disease?].

Truncus arteriosus is an uncommon heart malformation; it is not reported that recurrence is high; nevertheless authors report three families with two or more cases; in the third there is a very high consanguinity (two uncle-niece marriages). The authors compare the situation with hypoplastic left heart and think that some cases of truncus arteriosus would have an autosomal recessive inheritance. That is an another argument for suggesting an echocardiographic survey of the pregnancies in these families.

Consanguinity↗
PubMed1989

[Progressive pulmonary hypertension following repair of pseudotruncus arteriosus with major aorto-pulmonary collateral arteries in a 20-year-old patient].

External conduit operation was performed for a 20 year-old woman with pseudotruncus arteriosus with major aorto-pulmonary collateral arteries (MAPCAs). Immediate postoperative pulmonary to systemic peak pressure ratio was 0.70, and decreased to 0.53 on the second postoperative day. She had episodes of pulmonary hypertensive crisis soon after the operation, and injection of tolazoline hydrochloride was effective on them. Seven months after surgery, cardiac catheterization revealed severe pulmonary hypertension (PH) above the systemic level. Pulmonary arterial pressure did not respond to any drug nor to inhalation of oxygen. The progression of PH may be due to the pulmonary obstructive disease, and its causes were thought to be the repetition of constriction of pulmonary arterioles, hypoxia due to the giant bullae, diminished pulmonary vascular beds due to ligation of arborized MAPCAs, and relatively high age at operation.

Adult↗
PubMed1988

The fate of the 12 mm porcine valved conduit from the right ventricle to the pulmonary artery. A ten-year experience.

The 12 mm Dacron conduit containing a porcine valve is the smallest valved conduit manufactured and is used in the youngest infants with the most diminutive pulmonary arterial system. The outcome of patients with such a conduit is unknown. Between 1975 and 1985 there were 49 hospital survivors after placement of a 12 mm extracardiac valved conduit from the right ventricle to the pulmonary artery. Follow-up is available in 42 patients, aged 1 to 16 months (mean 3.5) and weighing 2.5 to 8.7 kg (mean 3.8). Twenty-eight patients (67%) have undergone subsequent conduit replacement, and 11 (26%) are alive and asymptomatic with a mean follow-up of 56 months. There were three late deaths. The interval between implantation and conduit change was 4.5 to 101 months (mean 44), allowing a weight gain of 2.7 to 23 kg (mean 10.4) before reoperation at age 12 to 117 months (mean 49). Despite elevated right ventricular pressures equaling systemic values, 37% of these patients were clinically asymptomatic. The gradient across the 12 mm valved conduit before explantation ranged from 30 to 173 torr (mean 83) with an almost equal predilection for stenosis at the proximal anastomosis, valve, conduit, distal anastomosis, and main pulmonary artery. The intervening pulmonary artery growth determined the size of the replacement conduit, 14 to 25 mm (mean 16), and was the main factor influencing the results of reoperation. This study demonstrates that the 12 mm porcine valve-containing conduit affords palliation in this difficult subset of patients with the smallest pulmonary arterial tree.

Bioprosthesis↗
PubMed1988

Dieulafoy's lesion associated with truncus arteriosus type IV: an unusual cause of upper gastrointestinal hemorrhage.

Dieulafoy's lesion is an abnormal submucosal artery in the stomach characterized by massive and often fatal upper gastrointestinal hemorrhage. Diagnosis is usually made at operation, as endoscopy and arteriography frequently fail to identify the lesion. Embolization may be helpful, but surgery is generally the treatment of choice. We present the first reported case of Dieulafoy's lesion in a 17-yr-old boy with type IV truncus arteriosus. This congenital cardiac anomaly may have predisposed this patient to early manifestation of Dieulafoy's lesion, a rare and frequently unrecognized disorder.

Adolescent↗