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Results for “MELORHEOSTOSIS”

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At least 109 records · Page 6Linked to original sources

PubMed1978

Melorheostosis. A case report with special reference to bone mineral density, bone circulation and bone scan.

A new case of melorheostosis is presented. Bone mineral density, and bone circulation were determined and bone scan carried out in the patient. The bone mineral density measured by photon absorption in the region of the distal radius of the patient's left forearm was found to be within normal limits, the bone blood circulation determined by Xc-133 clearance method was better in the affected side, and an area of increased uptake of Tc99m was found by bone scanning in the affected extremity.

Adult↗

PubMed1978

[Melorheostosis: study of a case (author's transl)].

The Authors describe a case of melorheostosis. The diagnosis, which is only radiological, is characteized by the tipical aspect of flowing hyperostosis.

Adolescent↗

PubMedDate not supplied

Melorheostosis of the hand: description of one case.

The authors describe a rare case of melorheostosis of the hand occurring at an early age but which was already present during early childhood. The patient came to our clinical observation only for cosmetic reasons. Because there were no other disorders no therapy was carried out.

Adolescent↗

PubMed1976

[Melorheostosis in adults. Apropos of 2 cases, 1 of them treated with diphosphonate (EHDP)].

The authors report two cases of melorheostosis discovered in adults because of fairly intense pain and deformation of the affected limb. The radiological appearances were typical. Isotope bone scintigraphy showed strong hyperfixation in the affected bones. A histomorphometric study of a double iliac bone biopsy showed on the one hand, cortical hypertrophy, normal osteonic architecture, and normal lamellar texture in the pathological regions, and, on the other hand, the dynamic character of the healthy bone close the lesions. In one of the patients an original attempt at treatment with diphosphonate (1 200 mg/day of EHDP for 5 months) resulted in a clear improvement in the bone pain. The disease is considered to be a mesodermic dystrophy. It seems to be due to strong hyperactivity of the subperiosteal bone accretion, which, normally, persists only at a weak level in adults.

Adult↗

PubMed1996

Unique cause of renovascular hypertension: melorheostosis associated with a malformation of the renal arteries.

We describe the case of a 17-year-old patient with melorheostosis and renovascular hypertension, an association that has not been reported before. Also the patient's aortic valve insufficiency could be attributed to underlying mesenchymal and vascular dysplasia.

Adolescent↗

PubMed1996

Melorheostosis of the hand.

We report a case of melorheostosis of the hand which showed a sclerotomal pattern of involvement, with swelling and pain. Surgical debulking resulted in correction of the deformity and relief of pain.

Adult↗

PubMed1998

Melorheostosis: complications of a tibial lengthening with the Ilizarov apparatus.

Melorheostosis is a rare bone dysplasia, exceptionally described in childhood. It has been discovered in a 12-year-old boy who had a hemimelic affection associated with straw-berry skin marks. A 25 mm inequality of length of the lower limbs and a valgus deformation of the ankle resulting in a claudication and gonalgia requiring surgical correction. A reaxation and a progressive lengthening with the Ilizarov apparatus has been performed. Non-consolidation and a secondary bone infection led to the necessity of formation of a soleus flap. Consolidation and healing were finally obtained. In addition to vascular complications to be feared in this disease during surgical treatment, we have to take into consideration the absence of consolidation when the osteotomy is not performed on a safe bone.

Child↗

PubMed1963