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Biomedical subjects

S Ariza

Publications and source records attributed to S Ariza.

15 recordsLinked to original sources

[Aortic coarctation in children. Analysis of 100 cases].

One hundred clinical records of coarctation of aorta are presented with 78% catheterization and 31% postmortem examination. Surgical treatment was performed in 46%, 8, in the first month of life, 13 from 1 to 6 month, 5, from 6 to 12 month, 9 from 12 to 24 month and 11 older than 2 years. The surgical mortality was 13%. There was recoarctation in 7.5%. The mortality in the patients not operated on was 31%. This mortality was influenced by the severity of associated malformations. The most frequent associated cardiac malformations were left to right shunts followed by left heart pathology. The association with complex cardiopathies was frequent.

Aortic Coarctation↗

[Clinicopathological correlations in the common atrioventricular canal].

20 patients with endocardial cushion defects were studied. Partial forms of common atrioventricular canal and those associated with complex congenital malformations were not considered. The right and left ventricular inflow and outflow tracts were measured and average values of inflow tract/outflow tract were calculated for each anatomical form of the disease. We found this ratio to be significantly smaller in Group B2 compared to Group B1 of Enriquez de Salamanca's classification, the first group being considered to be a more severe congenital malformation than the second. The inflow tract/outflow tract ratio of the right ventricle ranged between 80% and 50%, with an average of 62.3% in Group B1 compared to 62% and 24% with an average of 49% in Group B2. Using Studert's test, this difference was shown to be statistically significant (p = 0.02). On the other hand, there was no correlation between the other parameters or between the severity of the anatomical lesions and the clinical condition. The reduction of the right ventricular inflow tract may give an indication as to the type of atrioventricular valve which may be present.

Endocardium↗

Uhl's anomaly associated with pulmonary atresia.

We present a case of Uhl's anomaly associated with atresia of the pulmonary valve. The rarity of this association is noteworthy, only three cases having previously been published. Our case presents the peculiarity of a patient with a normal tricuspid valve.

Female↗

[Parachute tricuspid valve associated with Fallot's tetralogy].

Parachute deformity of the tricuspid valve was observed with a severe form of Fallot's Tetralogy with pulmonary atresia in a newborn. Signs of tricuspid stenosis (peripheral oedema, right atrial dilatation, hepatomegaly and conduction defects) were associated with the clinical signs of the principal malformation (severe hypoxaemia). To our knowledge, this is the first reported case of parachute deformity of the tricuspid valve.

Humans↗

[Right ventricle with double outlet and intact interventricular septum. Report of 1 case and review of the literature].

Double outlet right ventricle with an intact interventricular septum is an exceedingly rare malformation. Only six other cases have been found in the world literature. The clinical, electrocardiographic, radiological and anatomical features of this condition were reviewed on the occasion of the diagnosis of a new case. Cardiac catheterisation and angiography performed in only one other case is not definitive in the presence of mitral atresia.

Autopsy↗

Intracardiac heterotopia--mesenchymal and endodermal.

A case is reported of an intracardiac 'epithelial heterotopia' with a predominant mesenchymal component. This is thought to have resulted from the differentiation of aberrant primitive cell(s) displaced into the heart during its development. Though microscopically resembling a myxoma, this lesion is clearly distinguished by the presence of glandular structures. The myxoid component exhibited a startling invasiveness which resulted in occlusion of the superior vena cava, causing symptoms very early in life and death at the age of 6 months.

Choristoma↗

[Coarctation of the aorta. In infancy (author's transl)].

We review our experience in 38 patients with coarctation of the aorta during infancy. Cardiac failure was present in 30 patients, being the maximal incidence during the first and second weeks of the life. Sixteen infants died, 43% of them during the first week. Cardiac catherization and angiocardiography were performed in 22 infants. The coarctation of the aorta was isolated in 38 infants (36%). The most frequently associated malformations were: patent ductus arteriosus (6 cases), ventricular septal defect (5 cases) and the pathology of the left heart. The post mortem examination was performed in 11 infants; in all of them the CoAo was preductal with patent ductus arteriosus; the most frequently associated malformation was ventricular septal defect (6 cases). 5 infants were operated upon with succes during the first year of the life.

Angiocardiography↗

[Diagnostic of the heart tumors in newborn and children (author's transl)].

Heart tumors in children are rare. Though of benign pathology they are clinically malignant and should be diagnosed early and promptly treated by surgery in spite of the poor results usually obtained. Any heart enlargement in the absence of congenital heart disease accompanied by rhythm and conduction troubles must be considered as suspect. Five cases of heart tumor are reported and clinically described. Four occurred in newborns and the remaining one before the age of one. Heart enlargement was a constant finding. The ECG findings were: W.P.W. syndrome, intraventricular conduction troubles and ventricular tachycardia, wandering pacemaker (one case each) and ventricular hypertrophy with surprisingly low voltages in the corresponding chest leads (two cases).

Cardiomegaly↗