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PubMed · 637987

Intracardiac heterotopia--mesenchymal and endodermal.

S Ariza·E Rafel·J A Castillo·J A Garcia-Canton
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Abstract

A case is reported of an intracardiac 'epithelial heterotopia' with a predominant mesenchymal component. This is thought to have resulted from the differentiation of aberrant primitive cell(s) displaced into the heart during its development. Though microscopically resembling a myxoma, this lesion is clearly distinguished by the presence of glandular structures. The myxoid component exhibited a startling invasiveness which resulted in occlusion of the superior vena cava, causing symptoms very early in life and death at the age of 6 months.

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ChoristomaDiagnosis, DifferentialEndodermHeart NeoplasmsHumansInfantMaleMyxomaNeoplasm InvasivenessVena Cava, SuperiorCase ReportsJournal Article

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S Ariza, E Rafel, J A Castillo, J A Garcia-Canton. 1978. Intracardiac heterotopia--mesenchymal and endodermal.. https://doi.org/10.1136/hrt.40.3.325

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