Bifid epiglottis.

B Stroh; F L Rimell; N Mendelson

doi:10.1016/s0165-5876(98)00165-7

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PubMed · 10206398

Bifid epiglottis.

B Stroh·F L Rimell·N Mendelson

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Abstract

Bifid epiglottis is a rare congenital defect that is often associated with other congenital annomalies. The most common defect associated with a bifid epiglottis are anomalies of the hands and/or feet (90%) while the most dangerous and potentially lethal anomaly if not recognized and treated are hypothalamic hamartomas and hypopituitarism (50%). A bifid epiglottis will often result in severe respiratory distress secondary to laxity of the cartilage and chronic aspirations, which may require surgical intervention. We present the case of a 10-week-old child who was sent for evaluation of stridor and aspiration. Office laryngoscopy demonstrated a true bifid epiglottis and further evaluation demonstrated a hypothalamic hamartoma consistent with Pallister-Hall syndrome. Management of our case as well as those previously presented in the literature are reviewed.

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Child, Preschool Epiglottis Hamartoma Humans Hypopituitarism Hypothalamic Diseases Magnetic Resonance Imaging Male Pneumonia, Aspiration Polydactyly Respiratory Sounds Syndrome Case Reports Journal Article Review

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B Stroh, F L Rimell, N Mendelson. 1999-01-25. Bifid epiglottis.. https://doi.org/10.1016/s0165-5876(98)00165-7

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