Persistent hyperplastic primary vitreous with myopia: a case study.

G Steele; R Peters

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PubMed · 10547975

Persistent hyperplastic primary vitreous with myopia: a case study.

G Steele·R Peters

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Abstract

BACKGROUND: Persistent hyperplastic primary vitreous (PHPV) is a congenital disorder that manifests a range of ocular anomalies, including leukocoria, microphthalmia, cataract, and a retrolental fibrovascular membrane. In general, the prognosis for visual acuity with PHPV has been poor. A recent report on six patients who have myopia associated with PHPV showed that these patients were not microphthalmic, did not manifest leukocoria, and showed a mean visual acuity at final followup of 20/160. CASE REPORT: The case of a 3-year-old boy with myopic PHPV of the left eye is presented. Full-time wear of the cycloplegic refraction, combined with patching of the non-amblyopic eye, resulted in an improvement in visual acuity. RESULTS: PHPV with myopia may constitute a distinct subtype of PHPV. Patients with myopic PHPV tend to seek treatment later than patients with anterior or posterior PHPV as a result of the lack of microphthalmia and leukocoria. These individuals do not show the long-term complications, such as secondary glaucoma and intraocular hemorrhages, associated with PHPV. CONCLUSION: The acuity improvement in this case of myopic PHPV suggests that a more conservative approach to its surgical management may be appropriate while pursuing refractive correction and amblyopia therapy to attain the best acuity possible.

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Child, Preschool Diagnosis, Differential Eye Abnormalities Eye Hemorrhage Follow-Up Studies Glaucoma Humans Male Microphthalmos Myopia Refraction, Ocular Sensory Deprivation Visual Acuity Vitreous Body Case Reports Journal Article

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G Steele, R Peters. 1999. Persistent hyperplastic primary vitreous with myopia: a case study.. https://pubmed.ncbi.nlm.nih.gov/10547975/

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