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PubMed · 11684729

Active aortitis in relapsing polychondritis.

A G Selim·L G Fulford·R H Mohiaddin·M N Sheppard
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Abstract

Relapsing polychondritis (RP) is a rare inflammatory multiorgan disorder affecting cartilaginous structures and other connective tissues. Serious cardiovascular complications have been reported in patients with RP, the most frequent being aortic or mitral regurgitation and aortic aneurysms. Aortitis is a very rare complication. An unusual case of active aortitis in a patient with RP, despite intensive immunosuppressive treatment, is described with a special emphasis on the pathological findings.

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AortaAortic Valve InsufficiencyAortitisEchocardiographyFemaleHeart Valve Prosthesis ImplantationHumansMiddle AgedPolychondritis, RelapsingCase ReportsJournal ArticleReview

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A G Selim, L G Fulford, R H Mohiaddin, M N Sheppard. 2001. Active aortitis in relapsing polychondritis.. https://doi.org/10.1136/jcp.54.11.890

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