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Congenital arhinia.

L McGlone
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Abstract

Congenital absence of the nose or arhinia is a rare defect of embryogenesis, often associated with other anomalies. It is potentially a life-threatening condition and requires the presence of a highly skilled neonatal resuscitation team at the time of delivery. The associated anomalies often have a significant impact on the immediate as well as long-term outcome of the neonate. Parental counselling is thus vital and a multidisciplinary team approach is required to optimise the neonatal outcome. A neonate with congenital arhinia is reported and the literature reviewed to suggest guidelines for the management of such cases.

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HumansInfant, NewbornMaleNoseCase ReportsJournal Article

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BibTeXRIS

L McGlone. 2003. Congenital arhinia.. https://doi.org/10.1046/j.1440-1754.2003.00193.x

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