Microscopic polyangiitis associated with primary biliary cirrhosis.

Florenzo Iannone; Paola Falappone; Giovanni Pannarale; Antonietta Gentile; Vito Grattagliano; Michele Covelli; Giovanni Lapadula

PubMed · 14719218

Microscopic polyangiitis associated with primary biliary cirrhosis.

Florenzo Iannone·Paola Falappone·Giovanni Pannarale·Antonietta Gentile·Vito Grattagliano·Michele Covelli·Giovanni Lapadula

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Abstract

We describe a patient with microscopic polyangiitis and primary biliary cirrhosis (PBC) who presented with a non-erosive polyarthritis followed by pulmonary and renal involvement and signs of liver disorder. Detection of pANCA and antimitochondrial antibodies with results of renal and liver biopsies allowed a diagnosis of microscopic polyangiitis and PBC. To our knowledge, this is the first report of an association between the 2 diseases.

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Antibodies, Antineutrophil Cytoplasmic Biopsy Cyclophosphamide Female Humans Kidney Kidney Glomerulus Liver Liver Cirrhosis, Biliary Middle Aged Mitochondria, Liver Prednisone Treatment Outcome Vasculitis Case Reports Journal Article

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Florenzo Iannone, Paola Falappone, Giovanni Pannarale, Antonietta Gentile, Vito Grattagliano, Michele Covelli, Giovanni Lapadula. 2003. Microscopic polyangiitis associated with primary biliary cirrhosis.. https://pubmed.ncbi.nlm.nih.gov/14719218/

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