Pierre Robin sequence and double aortic arch: a case report.

Edward T Waters; James P Oberman; Abhik K Biswas

doi:10.1016/j.ijporl.2004.07.025

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Pierre Robin sequence and double aortic arch: a case report.

Edward T Waters·James P Oberman·Abhik K Biswas

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Abstract

We present an 8-day-old female with two admissions for respiratory failure. On the first admission, the diagnosis of Pierre Robin sequence (PRS) and laryngomalacia was made after assessment with chest radiography, echocardiography, and flexible fiberoptic laryngoscopy. Four days after discharge, the child presented with stridor and respiratory distress, and a new cardiac murmur was noted after admission. Repeat echocardiography, with confirmatory direct laryngobronchoscopy, revealed a double aortic arch (DAA) with distal tracheal compression. This case illustrates the necessity of a complete otolaryngic evaluation, including direct laryngobronchoscopy, to search for a synchronous airway lesion in any neonate with severe respiratory distress associated with stridor.

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Aorta, Thoracic Bronchoscopy Diagnosis, Differential Echocardiography, Doppler, Color Female Heart Defects, Congenital Humans Infant, Newborn Laryngeal Diseases Laryngoscopy Pierre Robin Syndrome Respiratory Insufficiency Respiratory Sounds Tomography, X-Ray Computed Case Reports Journal Article

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Edward T Waters, James P Oberman, Abhik K Biswas. 2005. Pierre Robin sequence and double aortic arch: a case report.. https://doi.org/10.1016/j.ijporl.2004.07.025

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