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Ventricular inversion with truncus arteriosus.

B Marino·L Ballerini·A Soro
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Abstract

We report clinical, angiocardiographic, and anatomic findings of an infant with ventricular inversion (atrioventricular discordance) and truncus arteriosus. The patient was in congestive heart failure and the injections into the left ventricle, right ventricle, and truncus arteriosus allowed a precise diagnosis. The autopsy confirmed this very unusual combination of anomalies and in particular it showed a truncus type 2 completely surrounded by muscular infundibulum and mainly aligned with the right ventricle. Surgical correction of this malformation is a challenge and so far, to our knowledge, has never been reported in the literature.

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Abnormalities, MultipleHeart VentriclesHumansInfantMaleTruncus Arteriosus, PersistentCase ReportsJournal Article

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BibTeXRIS

B Marino, L Ballerini, A Soro. 1990. Ventricular inversion with truncus arteriosus.. https://doi.org/10.1378/chest.98.1.239

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