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PubMed · 3545018

Infantile lobar emphysema.

N T Berlinger·D P Porto·T R Thompson
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Abstract

Infantile lobar emphysema is a symptom complex representing a spectrum of diseases characterized by overdistention of a pulmonary lobe by a check valve mechanism. The earlier in life infantile lobar emphysema presents, the more severe are the symptoms. Half of the cases appear in the first 4 weeks of life. The chest radiograph is the best diagnostic tool but can be misinterpreted. Computed tomography sometimes discloses the cause, which appears to be bronchial obstruction in 25% of cases. The bronchial obstruction may be due to intrinsic defects or to extrinsic compression. Bronchoscopy should be performed only in certain cases and then only with careful anesthetic management.

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BronchiBronchoscopyHumansInfantLungPneumonectomyPulmonary EmphysemaTerminology as TopicTomography, X-Ray ComputedJournal ArticleReview

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N T Berlinger, D P Porto, T R Thompson. Infantile lobar emphysema.. https://doi.org/10.1177/000348948709600124

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