[Hereditary fructose intolerance].

C Viscoli; G Ferrea; G Agnese; E Bertorello

PubMed · 6634433

[Hereditary fructose intolerance].

C Viscoli·G Ferrea·G Agnese·E Bertorello

Abstract

Two cases of hereditary fructose intolerance are reported. In the first one the symtomatology has started with an acute hepatic failure; the second one has come to our observation with a diagnosis of intrahepatic biliary duct atresia. It is underlined the difficulty of a differential diagnosis, in infants with serious hepatic failure, between infectious, metabolic and others illnesses.

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Bile Ducts, Intrahepatic Biopsy Carbohydrate Metabolism, Inborn Errors Female Fructose Intolerance Humans Infant Liver Liver Diseases Male Case Reports English Abstract Journal Article

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C Viscoli, G Ferrea, G Agnese, E Bertorello. [Hereditary fructose intolerance].. https://pubmed.ncbi.nlm.nih.gov/6634433/

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