[Reye's syndrome: pathogenetic problems (author's transl)].

G Sabetta; M Castro; A Donfrancesco; P Castelli; V Lucidi; R Lubrano; U Ruberto; M Qaddourah

PubMed · 7343954

[Reye's syndrome: pathogenetic problems (author's transl)].

G Sabetta·M Castro·A Donfrancesco·P Castelli·V Lucidi·R Lubrano·U Ruberto·M Qaddourah

Abstract

The authors describe six subjects with Reye's syndrome. All subjects died nevertheless the treatment (exchange-transfusions infusions of citrulline and ornithine). The autoptical studies showed cerebral oedema and fatty degeneration of the liver. Hepatic and seric OTC activity was measured in three patients: enzyme activity was virtually absent in one patient and normal in the other two. Instead in one patient was found partial CPS deficiency. However, Reye's syndrome is not only correlated with enzymatic deficiency of urea's cycle but sometimes also with toxic and metabolic causes.

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Child Child, Preschool Citrulline Exchange Transfusion, Whole Blood Female Humans Infant Male Ornithine Reye Syndrome English Abstract Journal Article

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G Sabetta, M Castro, A Donfrancesco, P Castelli, V Lucidi, R Lubrano, U Ruberto, M Qaddourah. [Reye's syndrome: pathogenetic problems (author's transl)].. https://pubmed.ncbi.nlm.nih.gov/7343954/

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