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Systemic vasculitis complicating infantile autoimmune enteropathy.

H R Jenkins·F Jewkes·G M Vujanic
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Abstract

An infant with unexplained sideroblastic anaemia and severe protracted diarrhoea due to autoimmune gut disease is reported. Despite treatment with an exclusion diet and immunosuppressive agents she developed a severe systemic vasculitic illness. Intensive treatment with plasmapheresis resulted in resolution of the vasculitic process but the child subsequently died after overwhelming septicaemia.

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Anemia, SideroblasticAutoimmune DiseasesFatal OutcomeFemaleHumansImmunosuppressive AgentsInfantIntestinal DiseasesPlasmapheresisSepsisVasculitisCase ReportsJournal Article

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BibTeXRIS

H R Jenkins, F Jewkes, G M Vujanic. 1994. Systemic vasculitis complicating infantile autoimmune enteropathy.. https://doi.org/10.1136/adc.71.6.534

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