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PubMed · 9176825

Diet does not ensure normal development in galactosemia.

K Widhalm·B D Miranda da Cruz·M Koch
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Abstract

This review deals with the treatment of inherited classical galactosemia by a lactose-free diet. Although, with dietary treatment, there is a remarkable improvement in the acute phase of the disease, the long-term outcome has been disappointing for most patients, especially regarding the central nervous system and ovarian dysfunction in females. There is a need for new approaches to treatment, in combination with diet therapy, that could improve the outcome of patients with galactosemia.

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BibTeXRIS

K Widhalm, B D Miranda da Cruz, M Koch. 1997. Diet does not ensure normal development in galactosemia.. https://doi.org/10.1080/07315724.1997.10718675

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