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Dermatofibrosarcoma protuberans in childhood.

M L Bouyssou-Gauthier·F Labrousse·B Longis·C Bedane·P Bernard·J M Bonnetblanc
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Abstract

Dermatofibrosarcoma protuberans (DFSP) is a rare cutaneous tumor with a possibly misleading presentation. It is rare in childhood. We report an 18-month-old child with an acquired atrophic plaque of the left ankle. Based on clinical findings, initial proposed diagnoses included localized scleroderma and localized lipoatrophy. At the age of 5 years the plaque had increased in size and become a purplish color. Several firm nodules were seen at its periphery. A diagnosis of DFSP was proposed and confirmed histologically. A large surgical resection was performed. This case illustrates that DFSP may occur in childhood, during which initial diagnosis is generally more difficult than in adulthood.

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Age FactorsAnkleBiopsyDermatofibrosarcomaHumansInfantMaleSkin NeoplasmsCase ReportsJournal Article

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M L Bouyssou-Gauthier, F Labrousse, B Longis, C Bedane, P Bernard, J M Bonnetblanc. Dermatofibrosarcoma protuberans in childhood.. https://doi.org/10.1111/j.1525-1470.1997.tb00691.x

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